ICD-11 code : 6D82;
Preferred Label : Dementia due to Lewy body disease;
ICD-11 definition : Dementia preceding or occurring within one year after the onset of motor parkinsonian
signs in the setting of Lewy body disease. Characterized by presence of Lewy bodies,
which are intraneuronal inclusions containing α-synuclein and ubiquitin in the brain
stem, limbic area, forebrain, and neocortex. Onset is insidious with attentional and
executive functioning deficits often present. These cognitive deficits are often accompanied
by visual hallucinations and symptoms of REM sleep behaviour disorder. Hallucinations
in other sensory modalities, depressive symptoms, and delusions may also be present.
The symptom presentation usually varies significantly over the course of days necessitating
longitudinal assessment and differentiation from delirium. Spontaneous onset of Parkinsonism
within approximately 1 year of the onset of cognitive symptoms is common.;
ICD-11 synonym : senile dementia of the lewy body type; dementia of the lewy body type; SDLT - [senile dementia of the lewy body type]; dementia with lewy bodies;
ICD-11 acronym : SDLT;
Origin ID : 1777436789;
Currated CISMeF NLP mapping
Dementia preceding or occurring within one year after the onset of motor parkinsonian
signs in the setting of Lewy body disease. Characterized by presence of Lewy bodies,
which are intraneuronal inclusions containing α-synuclein and ubiquitin in the brain
stem, limbic area, forebrain, and neocortex. Onset is insidious with attentional and
executive functioning deficits often present. These cognitive deficits are often accompanied
by visual hallucinations and symptoms of REM sleep behaviour disorder. Hallucinations
in other sensory modalities, depressive symptoms, and delusions may also be present.
The symptom presentation usually varies significantly over the course of days necessitating
longitudinal assessment and differentiation from delirium. Spontaneous onset of Parkinsonism
within approximately 1 year of the onset of cognitive symptoms is common.
