" /> peroxisomal bifunctional enzyme - CISMeF





Preferred Label : peroxisomal bifunctional enzyme;

MeSH definition : A monomeric protein found in liver peroxisomes that contains two enzymatically active domains; an enoyl-CoA hydratase/3,2-trans-enoyl-CoA isomerase domain, and an (S)-3-hydroxyacyl-CoA dehydrogenase domain. The enzyme is stereospecific with regards to how cis and trans double bonds are metabolized. It is complemented by PEROXISOMAL MULTIFUNCTIONAL PROTEIN-2, which has the opposite stereospecificity.;

MeSH synonym : bifunctional enzyme, peroxisomal; enoyl CoA hydratase 3 hydroxyacyl CoA dehydrogenase; Peroxisomal-Bifunctional enzymes; peroxisomal bifunctional enzymes; L-Peroxisomal bifunctional enzyme; bifunctional enzyme, L-Peroxisomal; L peroxisomal bifunctional enzyme; peroxisomal hydratase dehydrogenase epimerase; peroxisomal multifunctional beta-Oxidation protein; peroxisomal multifunctional beta oxidation protein; peroxisomal trifunctional enzyme; 2-Enoyl-CoA hydratase, 3-Hydroxyacyl-CoA dehydrogenase-delta 3, delta 2-Enoyl-CoA isomerase; L-Bifunctional enzyme; L bifunctional enzyme; Peroxisomal Hydratase-Dehydrogenase-Epimerase; Hydratase-Dehydrogenase-Epimerase, Peroxisomal; Enoyl-CoA Hydratase-3-Hydroxyacyl-CoA Dehydrogenase; Dehydrogenase, Enoyl-CoA Hydratase-3-Hydroxyacyl-CoA; Hydratase-3-Hydroxyacyl-CoA Dehydrogenase, Enoyl-CoA;

CISMeF synonym : Enoyl-CoA hydratase -- 3-Hydroxyacyl-CoA dehydrogenase; delta(3), delta(2)-Enoyl-CoA isomerase; 2-Enoyl-CoA hydratase; 3-Hydroxyacyl-CoA dehydrogenase; peroxisomal hydratase - dehydrogenase - epimerase;

MeSH Related Number : EC 1.1.1.35; EC 5.3.3.8;

Registry Number MeSH : EC 4.2.1.17;

Is substance : O;

UNII : EC 4.2.1.17;

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A monomeric protein found in liver peroxisomes that contains two enzymatically active domains; an enoyl-CoA hydratase/3,2-trans-enoyl-CoA isomerase domain, and an (S)-3-hydroxyacyl-CoA dehydrogenase domain. The enzyme is stereospecific with regards to how cis and trans double bonds are metabolized. It is complemented by PEROXISOMAL MULTIFUNCTIONAL PROTEIN-2, which has the opposite stereospecificity.

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08/06/2025


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