Preferred Label : craniopharyngioma;
RADLEX synonyms : craniopharyngioma (WHO grade I);
Definition : A benign pituitary-region neoplasm that originates from Rathke's pouch. The two major
histologic and clinical subtypes are adamantinous (or classical) craniopharyngioma
and papillary craniopharyngioma. The adamantinous form presents in children and adolescents
as an expanding cystic lesion in the pituitary region. The cystic cavity is filled
with a black viscous substance and histologically the tumor is composed of adamantinomatous
epithelium and areas of calcification and necrosis. Papillary craniopharyngiomas occur
in adults, and histologically feature a squamous epithelium with papillations. (From
Joynt, Clinical Neurology, 1998, Ch14, p50) [MeSH];
UMLS CUI (RADLEX) : C0010276;
Origin ID : RID4147;
UMLS CUI : C0010276;
Automatic exact mappings (from CISMeF team)
- Semantic type(s)
- UMLS correspondences (same concept)
A benign pituitary-region neoplasm that originates from Rathke's pouch. The two major
histologic and clinical subtypes are adamantinous (or classical) craniopharyngioma
and papillary craniopharyngioma. The adamantinous form presents in children and adolescents
as an expanding cystic lesion in the pituitary region. The cystic cavity is filled
with a black viscous substance and histologically the tumor is composed of adamantinomatous
epithelium and areas of calcification and necrosis. Papillary craniopharyngiomas occur
in adults, and histologically feature a squamous epithelium with papillations. (From
Joynt, Clinical Neurology, 1998, Ch14, p50) [MeSH]
