Preferred Label : Craniopharyngioma;
NCIt synonyms : Rathke Pouch Neoplasm; Craniopharyngioma (WHO Grade I); Rathke's Pouch Neoplasm; Rathke Pouch Tumor; Craniopharyngioma (WHO Grade 1); Tumor of Rathke's Pouch;
NCIt related terms : Neoplasm of Rathke's Pouch; Rathke's Pouch Tumor; CRANIOPHARYNGIOMA, BENIGN; Cystoma; Benign neoplasm of craniopharyngeal duct; Craniopharyngeal Tumor;
NCIt definition : A benign, partly cystic, epithelial tumor of the sellar region, presumably derived
from Rathke pouch epithelium. It affects mainly children and young adults. There are
two clinicopathological forms: adamantinomatous craniopharyngioma and papillary craniopharyngioma.
The most significant factor associated with recurrence is the extent of surgical resection,
with lesions greater than 5 cm in diameter carrying a markedly worse prognosis. (Adapted
from WHO);
Alternative definition : NICHD: A histologically benign, but locally destructive, partly cystic, epithelial
tumor of the sellar region, derived from Rathke pouch epithelium.; CDISC: A benign epithelial neoplasm of the sellar region, presumably derived from
Rathke pouch epithelium.; NCI-GLOSS: A benign brain tumor that may be considered malignant because it can damage
the hypothalamus, the area of the brain that controls body temperature, hunger, and
thirst.;
Neoplastic status : Benign;
ICD-O code : 9350/1;
Codes from synonyms : 10011318; CDR0000046131; D35.3;
Origin ID : C2964;
UMLS CUI : C0010276;
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
DO Cross reference
Disease excludes abnormal cell
Disease excludes normal cell origin
Disease may have findings
Excludes anatomical site(s)
False automatic mappings
Has associated anatomic sites
Semantic type(s)
UMLS correspondences (same concept)
concept_is_in_subset
disease_excludes_finding
disease_has_abnormal_cell
disease_has_associated_disease
disease_has_finding
disease_has_grade
disease_has_normal_cell_origin
disease_has_normal_tissue_origin
disease_has_primary_anatomic_site
disease_may_have_associated_disease