IgG4-Related Disease

Preferred Label : IgG4-Related Disease;

NCIt synonyms : IgG4-Related Sclerosing Disease; IgG4RD;

NCIt definition : An uncommon, mass-forming lesion that affects single or multiple sites. It is characterized by the presence of a lymphoplasmacytic infiltrate rich in IgG4-positive plasma cells and storiform tissue fibrosis, and increased serum IgG4 levels. It usually occurs in the pancreas, submandibular glands, lacrimal glands, lymph nodes, and hepatobiliary tract. Patients usually present with fatigue and weight loss. It responds to steroids treatment and follows a course of remissions and recurrences.;

Details

Origin ID

C95992;

UMLS CUI

C3203653;

Automatic exact mappings (from CISMeF team)
- IgG4-Related Sclerosing Disease [MeSH concept]
- IgG4-related disease [DO Concept]
- IgG4-related systemic disease [ORDO Disease]
- Immunoglobulin G4 related disease (disorder) [SNOMED CT concept]
- Immunoglobulin G4 related sclerosing disease [MedDRA LLT]
- Immunoglobulin G4-Related Disease [MeSH Descriptor]
Currated CISMeF NLP mapping
- IgG4 related sclerosing disease [MedDRA LLT]
- IgG4-related disease [ORDO Disease]
- Immunoglobulin G4 related sclerosing disease [MedDRA Preferred Term]
- immunoglobulin G4 related sclerosing disease [Disease (Nov.)]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
UMLS correspondences (same concept)
- IgG4 related sclerosing disease [MedDRA LLT]
- IgG4-related disease [ORDO Disease]
- Immunoglobulin G4 related sclerosing disease [MedDRA Preferred Term]
- Immunoglobulin G4 related sclerosing disease [MedDRA LLT]
- immunoglobulin G4 related sclerosing disease [Disease (Nov.)]
concept_is_in_subset
- Cellosaurus Disease Terminology [NCIt concept]
- Cellosaurus Terminology [NCIt concept]

Keyword's position in hierarchy(ies) :

You can consult :

recommendations
documents concerning education
documents for patients