Preferred Label : Immunoglobulin G4-Related Disease;
MeSH definition : A spectrum of systemic autoimmune diseases in which IMMUNOGLOBULIN G4 plays a pathophysiologic
role. It can affect multiple organs in highly variable presentations, characterized
by inflammatory lesions composed of IgG4-positive PLASMA CELLS, further infiltrated
by T helper cells (T-LYMPHOCYTES, HELPER-INDUCER) when linked to progressive FIBROSIS
and eventual organ damage.;
MeSH synonym : Immunoglobulin G4 Related Disease; Immunoglobulin G4-Related Diseases; IgG4 Related Systemic Disease; IgG4-RD; IgG4-Associated Autoimmune Disease; Autoimmune Disease, IgG4-Associated; IgG4 Associated Autoimmune Disease; IgG4-Associated Autoimmune Diseases; IgG4-Related Disease; IgG4 Related Disease; IgG4-Related Diseases;
CISMeF synonym : Autoimmune Diseases, IgG4-Associated; G4-Related Disease, Immunoglobulin; G4-Related Diseases, Immunoglobulin;
MeSH hyponym : IgG4 Related Sclerosing Disease; IgG4-Related Sclerosing Diseases; Sclerosing Disease, IgG4-Related; Immunoglobulin G4-Related Sclerosing Disease; Immunoglobulin G4 Related Sclerosing Disease;
Related MeSH term : IgG4 Related Kidney Disease; IgG4-Related Kidney Diseases; Kidney Disease, IgG4-Related; Immunoglobulin G4-Related Kidney Disease; Immunoglobulin G4 Related Kidney Disease;
Origin ID : D000077733;
UMLS CUI : C4087124;
Allowable qualifiers
Automatic exact mappings (from CISMeF team)
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See also
Semantic type(s)
UMLS correspondences (same concept)
Validated automatic mappings to BTNT
A spectrum of systemic autoimmune diseases in which IMMUNOGLOBULIN G4 plays a pathophysiologic
role. It can affect multiple organs in highly variable presentations, characterized
by inflammatory lesions composed of IgG4-positive PLASMA CELLS, further infiltrated
by T helper cells (T-LYMPHOCYTES, HELPER-INDUCER) when linked to progressive FIBROSIS
and eventual organ damage.