Follicular Dendritic Cell Sarcoma

Preferred Label : Follicular Dendritic Cell Sarcoma;

NCIt synonyms : Follicular Dendritic Cell Sarcoma/Tumor; FDCS;

NCIt related terms : Follicular dendritic cell tumor;

NCIt definition : A neoplasm composed of spindle to ovoid cells which have morphologic and immunophenotypic characteristics of follicular dendritic cells. It affects lymph nodes and other sites including the tonsils, gastrointestinal tract, spleen, liver, soft tissues, skin, and oral cavity. It usually behaves as a low grade sarcoma. Treatment options include complete surgical removal of the tumor with or without adjuvant chemotherapy or radiotherapy. Recurrences have been reported in up to half of the cases.;

Neoplastic status : Malignant;

ICD-O code : 9758/1; 9758/3;

Details

Origin ID

C9281;

UMLS CUI

C1260325;

Currated CISMeF NLP mapping
- Follicular dendritic cell sarcoma [MedDRA Preferred Term]
- Follicular dendritic cell sarcoma [ICD-O code]
- Follicular dendritic cell sarcoma [ICD-11 Extension code]
- Follicular dendritic cell sarcoma [ICD-11 Subcategory]
- Follicular dendritic cell sarcoma [ORDO Disease]
- Follicular dendritic cell sarcoma (morphologic abnormality) [SNOMED CT concept]
- dendritic cell sarcoma, follicular [MeSH Descriptor]
- dendritic cell sarcoma, follicular [MeSH concept]
- follicular dendritic cell sarcoma [Disease (Nov.)]
- follicular dendritic cell sarcoma [DO Concept]
DO Cross reference
- follicular dendritic cell sarcoma [DO Concept]
Disease excludes normal cell origin
- Epithelial Cell [NCIt concept]
Disease may have findings
- Asymptomatic Mass [NCIt concept]
- CD21-Positive Neoplastic Cells Present [NCIt concept]
- CD35-Positive Neoplastic Cells Present [NCIt concept]
- CD68-Positive Neoplastic Cells Present [NCIt concept]
- Indolent Clinical Course [NCIt concept]
- Lymphadenopathy [NCIt concept]
- S-100-Positive Neoplastic Cells Present [NCIt concept]
Has associated anatomic sites
- Connective and Soft Tissue [NCIt concept]
- Hematopoietic and Lymphatic System [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Follicular dendritic cell sarcoma [ORDO Disease]
- Follicular dendritic cell sarcoma [MedDRA Preferred Term]
- Follicular dendritic cell sarcoma [ICD-O code]
- Follicular dendritic cell sarcoma (morphologic abnormality) [SNOMED CT concept]
- dendritic cell sarcoma, follicular [MeSH concept]
- dendritic cell sarcoma, follicular [MeSH Descriptor]
- follicular dendritic cell sarcoma [DO Concept]
- follicular dendritic cell sarcoma [Disease (Nov.)]
Validated automatic mappings to NTBT
- Sarcoma of dendritic cells (accessory cells) [ICD-10 Sub-category]
- dendritic cell sarcoma [DO Concept]
concept_is_in_subset
- CPTAC Codelists Terminology [NCIt concept]
- CPTAC Neoplasms Codelist [NCIt concept]
- CPTAC Terminology [NCIt concept]
- CTRP Disease Terminology [NCIt concept]
- CTRP Terminology [NCIt concept]
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology Terminology [NCIt concept]
- Mapped ICDO3.1 Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
- NCIt Neoplasm Core Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Birbeck Granules Present [NCIt concept]
- CD1a-Positive Neoplastic Cells Present [NCIt concept]
- CD30-Positive Neoplastic Cells Present [NCIt concept]
- HMB-45-Positive Neoplastic Cells Present [NCIt concept]
- Indolent Clinical Course [NCIt concept]
- Intermediate Filaments Present [NCIt concept]
- Intracytoplasmic Eosinophilic Inclusion [NCIt concept]
disease_excludes_molecular_abnormality
- Clonal Immunoglobulin Gene Rearrangement [NCIt concept]
- Clonal T-Cell Receptor Gene Rearrangement [NCIt concept]
disease_excludes_normal_tissue_origin
- Epithelial Tissue [NCIt concept]
disease_has_abnormal_cell
- Malignant Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Follicular Dendritic Cell [NCIt concept]
- Neoplastic Hematopoietic and Lymphoid Cell [NCIt concept]
- Neoplastic Histiocytic and Dendritic Cell [NCIt concept]
- Neoplastic Spindle Cell [NCIt concept]
disease_has_finding
- Histiocytosis [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Rare Lesion [NCIt concept]
- Storiform Growth Pattern [NCIt concept]
- Whorling Growth Pattern [NCIt concept]
disease_has_normal_cell_origin
- Follicular Dendritic Cell [NCIt concept]
- Hematopoietic and Lymphoid Cell [NCIt concept]
- Histiocyte [NCIt concept]
- Histiocytic and Dendritic Cell [NCIt concept]
disease_has_normal_tissue_origin
- Connective and Soft Tissue [NCIt concept]
- Germinal Center [NCIt concept]
- Hematopoietic and Lymphoid Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Hematopoietic and Lymphatic System [NCIt concept]
disease_may_have_associated_disease
- Castleman Disease [NCIt concept]
disease_may_have_molecular_abnormality
- BRAF Gene Mutation [NCIt concept]

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