Pulmonary Alveolar Proteinosis

Preferred Label : Pulmonary Alveolar Proteinosis;

NCIt definition : A rare lung disorder characterized by the filling of the pulmonary alveoli with proteinaceous material which stains positive with periodic acid-Schiff stain. It may be idiopathic or secondary due to hematologic malignancies or the inhalation of mineral dusts. Signs and symptoms include dyspnea, cough and low grade fever.;

Details

Origin ID

C85037;

UMLS CUI

C0034050;

Automatic exact mappings (from CISMeF team)
- Autoimmune pulmonary alveolar proteinosis [ICD-11 More detail]
- Intraalveolar phospholipid accumulation [HPO term]
- Pulmonary alveolar proteinosis [ACR pathology]
Currated CISMeF NLP mapping
- Alveolar proteinosis [MedDRA Preferred Term]
- Autoimmune pulmonary alveolar proteinosis [ORDO Disease]
- Pulmonary alveolar proteinosis [ICD-9 code]
- Pulmonary alveolar proteinosis [PASCAL descriptor]
- Pulmonary alveolar proteinosis [ICD-11 Sub-sub category]
- Pulmonary alveolar proteinosis [MedDRA LLT]
- Pulmonary alveolar proteinosis (disorder) [SNOMED CT concept]
- pulmonary alveolar proteinosis [Radlex concept]
- pulmonary alveolar proteinosis [DO Concept]
- pulmonary alveolar proteinosis [Disease (Nov.)]
- pulmonary alveolar proteinosis [MeSH Descriptor]
- pulmonary alveolar proteinosis [MeSH concept]
- pulmonary alveolar proteinosis [SNOMED Notion]
DO Cross reference
- pulmonary alveolar proteinosis [DO Concept]
Has associated anatomic sites
- Lung [NCIt concept]
- Respiratory System [NCIt concept]
- Thoracic Cavity [NCIt concept]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
UMLS correspondences (same concept)
- Alveolar proteinosis [MedDRA Preferred Term]
- Intraalveolar phospholipid accumulation [HPO term]
- Pulmonary alveolar proteinosis [ICD-9 code]
- Pulmonary alveolar proteinosis [PASCAL descriptor]
- Pulmonary alveolar proteinosis [MedDRA LLT]
- Pulmonary alveolar proteinosis (disorder) [SNOMED CT concept]
- pulmonary alveolar proteinosis [Radlex concept]
- pulmonary alveolar proteinosis [DO Concept]
- pulmonary alveolar proteinosis [Disease (Nov.)]
- pulmonary alveolar proteinosis [MeSH concept]
- pulmonary alveolar proteinosis [MeSH Descriptor]
- pulmonary alveolar proteinosis [SNOMED Notion]
disease_has_finding
- Rare Lesion [NCIt concept]

Keyword's position in hierarchy(ies) :

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