ICD-11 code : CB04.31;
Preferred Label : Pulmonary alveolar proteinosis;
ICD-11 definition : This is a rare lung disease in which abnormal accumulation of surfactant occurs within
the alveoli, interfering with gas exchange. PAP can occur in a primary form or secondarily
in the settings of malignancy (especially in myeloid leukemia), pulmonary infection,
or environmental exposure to dusts or chemicals.;
Origin ID : 1869739196;
Currated CISMeF NLP mapping
ICD-10 Mapping
This is a rare lung disease in which abnormal accumulation of surfactant occurs within
the alveoli, interfering with gas exchange. PAP can occur in a primary form or secondarily
in the settings of malignancy (especially in myeloid leukemia), pulmonary infection,
or environmental exposure to dusts or chemicals.