" /> Diffuse Cerebral Sclerosis of Schilder - CISMeF





Preferred Label : Diffuse Cerebral Sclerosis of Schilder;

NCIt related terms : Diffuse sclerosis of central nervous system;

NCIt definition : A rare congenital demyelinating disorder affecting the central nervous system. It is characterized by a demyelinating destructive lesion affecting an entire brain lobe or hemisphere. Signs and symptoms include dementia, cortical deafness and blindness, pseudobulbar palsy, and hemiplegia.;

Codes from synonyms : G37.0;

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28/07/2025


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