Childhood Malignant Peripheral Nerve Sheath Tumor

Preferred Label : Childhood Malignant Peripheral Nerve Sheath Tumor;

NCIt synonyms : Pediatric Malignant Neoplasm of Peripheral Nerve Sheath; Pediatric Malignant Peripheral Nerve Sheath Tumor; Childhood Malignant Neoplasm of the Peripheral Nerve Sheath; Childhood Malignant Peripheral Nerve Sheath Neoplasm; Pediatric Malignant Tumor of Peripheral Nerve Sheath; Childhood Malignant Tumor of the Peripheral Nerve Sheath; Childhood Malignant Neoplasm of Peripheral Nerve Sheath; Pediatric Malignant Neurilemmoma; Pediatric MPNST; Childhood MPNST; Pediatric Malignant Neoplasm of the Peripheral Nerve Sheath; Childhood Malignant Tumor of Peripheral Nerve Sheath; Pediatric Malignant Tumor of the Peripheral Nerve Sheath; Childhood Malignant Schwannoma; Pediatric Malignant Peripheral Nerve Sheath Neoplasm; Pediatric Malignant Schwannoma;

NCIt related terms : Childhood Neurogenic Sarcoma; Childhood Malignant Neurilemmoma; Childhood Neurofibrosarcoma; Malignant Peripheral Nerve Sheath Tumor;

Alternative definition : NICHD: A malignant peripheral nerve sheath tumor occurring in children.;

Neoplastic status : Malignant;

Details

Origin ID

C8094;

UMLS CUI

C0279987;

Automatic exact mappings (from CISMeF team)
- Malignant peripheral nerve sheath tumor [MedDRA LLT]
- Malignant peripheral nerve sheath tumor [ICD-O code]
- Malignant peripheral nerve sheath tumor [ORDO Disease]
- Malignant peripheral nerve sheath tumor (disorder) [SNOMED CT concept]
- Malignant peripheral nerve sheath tumor (morphologic abnormality) [SNOMED CT concept]
- Neurofibrosarcoma [HPO term]
- Peripheral nerve sheath tumor malignant [MedDRA LLT]
- childhood malignant schwannoma [DO Concept]
- malignant peripheral nerve sheath tumor [DO Concept]
- malignant peripheral nerve sheath tumor [Radlex concept]
- malignant peripheral nerve sheath tumors [MeSH concept]
- neurilemmoma [MeSH Descriptor]
- neurofibrosarcoma [MeSH Descriptor]
DO Cross reference
- childhood malignant schwannoma [DO Concept]
Disease excludes normal cell origin
- Epithelial Cell [NCIt concept]
Disease may have findings
- Aggressive Clinical Course [NCIt concept]
- Geographic Necrosis [NCIt concept]
Has associated anatomic sites
- Connective and Soft Tissue [NCIt concept]
- Nervous System [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- childhood malignant schwannoma [DO Concept]
concept_is_in_subset
- CTRP Disease Terminology [NCIt concept]
- CTRP Terminology [NCIt concept]
- NICHD Terminology [NCIt concept]
- Pediatric Hematology-Oncology Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Indolent Clinical Course [NCIt concept]
- Intermediate Filaments Present [NCIt concept]
- Intracytoplasmic Eosinophilic Inclusion [NCIt concept]
disease_excludes_normal_tissue_origin
- Epithelial Tissue [NCIt concept]
disease_has_abnormal_cell
- Hyperchromatic Spindle Cell [NCIt concept]
- Malignant Cell [NCIt concept]
- Malignant Perineural Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Neuroepithelial Cell and Neoplastic Perineural Cell [NCIt concept]
- Neoplastic Perineural Cell [NCIt concept]
disease_has_finding
- Childhood Lesion [NCIt concept]
- Diffuse Pattern [NCIt concept]
- Firm Mass [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Necrotic Change [NCIt concept]
- Pseudoencapsulated Mass [NCIt concept]
disease_has_normal_cell_origin
- Neuron, Neuroepithelial Cell, and Supporting Cell of the Nervous System [NCIt concept]
- Perineural Cell [NCIt concept]
disease_has_normal_tissue_origin
- Connective and Soft Tissue [NCIt concept]
- Nerve Tissue and Nerve Sheaths [NCIt concept]
- Nerve Tissue, Neuroepithelial Tissue, and Nerve Sheaths [NCIt concept]
disease_has_primary_anatomic_site
- Peripheral Nerve [NCIt concept]
disease_may_have_associated_disease
- Neurofibromatosis Type 1 [NCIt concept]
disease_may_have_cytogenetic_abnormality
- Loss of Chromosome 22 [NCIt concept]
disease_may_have_molecular_abnormality
- TP53 Gene Inactivation [NCIt concept]

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