neurofibrosarcoma

Preferred Label : neurofibrosarcoma;

MeSH definition : A malignant tumor that arises from small cutaneous nerves, is locally aggressive, and has a potential for metastasis. Characteristic histopathologic features include proliferating atypical spindle cells with slender wavy and pointed nuclei, hypocellular areas, and areas featuring organized whorls of fibroblastic proliferation. The most common primary sites are the extremities, retroperitoneum, and trunk. These tumors tend to present in childhood, often in association with NEUROFIBROMATOSIS 1. (From DeVita et al., Cancer: Principles & Practice of Oncology, 5th ed, p1662; Mayo Clin Proc 1990 Feb;65(2):164-72);

MeSH synonym : neurogenic sarcoma; neurofibrosarcomas; sarcoma, neurogenic; neurogenic sarcomas; sarcomas, neurogenic;

MeSH hyponym : Neurilemmosarcoma; Neurilemmosarcomas; MPNST; Malignant Neurilemmoma; Malignant Neurilemmomas; Neurilemmoma, Malignant; Peripheral Nerve Sheath Tumors, Malignant; Malignant Neurilemoma; Malignant Neurilemomas; Neurilemoma, Malignant; Schwannoma, Malignant; Malignant Schwannoma; Malignant Schwannomas; Malignant Peripheral Nerve Sheath Tumor;

MeSH annotation : coordinate IM with precoordinated organ/neoplasm term (IM);

Wikipedia link : https://en.wikipedia.org/wiki/Malignant peripheral nerve sheath tumor;

Details

Origin ID

D018319;

UMLS CUI

C0206729;

Allowable qualifiers
- blood [MeSH Qualifier]
- blood supply [MeSH Qualifier]
- cerebrospinal fluid [MeSH Qualifier]
- chemically induced [MeSH Qualifier]
- chemistry [MeSH Qualifier]
- classification [MeSH Qualifier]
- complications [MeSH Qualifier]
- congenital [MeSH Qualifier]
- diagnosis [MeSH Qualifier]
- diagnostic imaging [MeSH Qualifier]
- diet therapy [MeSH Qualifier]
- drug therapy [MeSH Qualifier]
- economics [MeSH Qualifier]
- embryology [MeSH Qualifier]
- enzymology [MeSH Qualifier]
- epidemiology [MeSH Qualifier]
- ethnology [MeSH Qualifier]
- etiology [MeSH Qualifier]
- genetics [MeSH Qualifier]
- history [MeSH Qualifier]
- immunology [MeSH Qualifier]
- metabolism [MeSH Qualifier]
- microbiology [MeSH Qualifier]
- mortality [MeSH Qualifier]
- nursing [MeSH Qualifier]
- parasitology [MeSH Qualifier]
- pathology [MeSH Qualifier]
- physiopathology [MeSH Qualifier]
- prevention and control [MeSH Qualifier]
- psychology [MeSH Qualifier]
- radiotherapy [MeSH Qualifier]
- rehabilitation [MeSH Qualifier]
- secondary [MeSH Qualifier]
- surgery [MeSH Qualifier]
- therapy [MeSH Qualifier]
- ultrastructure [MeSH Qualifier]
- urine [MeSH Qualifier]
- veterinary [MeSH Qualifier]
- virology [MeSH Qualifier]
Automatic exact mappings (from CISMeF team)
- Adult Malignant Peripheral Nerve Sheath Tumor [NCIt concept]
- Cardiac Malignant Peripheral Nerve Sheath Tumor [NCIt concept]
- Childhood Malignant Peripheral Nerve Sheath Tumor [NCIt concept]
- Glandular Malignant Peripheral Nerve Sheath Tumor [NCIt concept]
- Malignant Peripheral Nerve Sheath Tumor of the Skin [NCIt concept]
- Malignant peripheral nerve sheath tumour [ICD-11 Extension code]
- Malignant peripheral nerve sheath tumour of cranial or paraspinal nerves [ICD-11 Sub-sub category]
- Metastatic Malignant Peripheral Nerve Sheath Tumor [NCIt concept]
- Neurilemmoma, malignant [ICD-9 code]
- Neurilemoma, malignant [ICD-11 Extension code]
- Neurofibrosarcoma [PASCAL descriptor]
- Neurofibrosarcoma [ICD-9 code]
- Sinonasal Malignant Peripheral Nerve Sheath Tumor [NCIt concept]
- malignant peripheral nerve sheath tumor [Radlex concept]
- neurofibrosarcoma [DO Concept]
Currated CISMeF NLP mapping
- Malignant peripheral nerve sheath tumor [ICD-O code]
- Malignant peripheral nerve sheath tumor [ORDO Disease]
- Malignant peripheral nerve sheath tumor [MedDRA LLT]
- Malignant peripheral nerve sheath tumor (disorder) [SNOMED CT concept]
- Malignant peripheral nerve sheath tumor (morphologic abnormality) [SNOMED CT concept]
- Malignant peripheral nerve sheath tumour [MedDRA LLT]
- Neurilemmoma malignant [MedDRA LLT]
- Neurilemmoma, malignant [ICD-O code]
- Neurilemoma malignant [MedDRA LLT]
- Neurilemoma, malignant (morphologic abnormality) [Inactive SNOMED CT concept]
- Neurofibrosarcoma [HPO term]
- Neurofibrosarcoma [MedDRA Preferred Term]
- Neurofibrosarcoma NOS [MedDRA LLT]
- Neurofibrosarcomas [MedDRA High Level Term]
- Peripheral nerve sheath tumor malignant [MedDRA LLT]
- Peripheral nerve sheath tumour malignant [MedDRA LLT]
- Schwannoma malignant [MedDRA LLT]
- malignant peripheral nerve sheath tumor [DO Concept]
- neurilemmoma, malignant [SNOMED Notion]
- neurofibrosarcoma [SNOMED Notion]
DO Cross reference
- malignant peripheral nerve sheath tumor [DO Concept]
- neurofibrosarcoma [DO Concept]
HPO term
- Neurofibrosarcoma [HPO term]
Record concept(s)
- malignant peripheral nerve sheath tumors [MeSH concept]
- neurofibrosarcoma [MeSH concept]
See also inter- (CISMeF)
- Malignant Peripheral Nerve Sheath Tumor [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Neurofibrosarcoma [MedDRA Preferred Term]
- Neurofibrosarcoma [HPO term]
- Neurofibrosarcoma NOS [MedDRA LLT]
- Neurofibrosarcomas [MedDRA High Level Term]
- Neurosarcoma [MedDRA LLT]
- neurofibrosarcoma [DO Concept]
- neurofibrosarcoma [SNOMED Notion]

Keyword's position in hierarchy(ies) :

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