Preferred Label : Subcutaneous Panniculitis-Like T-Cell Lymphoma;
NCIt synonyms : Subcutaneous Panniculitis-Like T-Cell Lymphoma (Alpha/Beta Type); Subcutaneous Panniculitis-Like T-Cell Lymphoma, Alpha/Beta Type; SPTCL;
NCIt definition : A cytotoxic primary cutaneous T-cell lymphoma. Recent studies suggest there are at
least two groups of subcutaneous panniculitis-like T-cell lymphomas, each with distinct
histologic features, immunophenotypic profile, and prognosis. One group has an alpha/beta,
CD8 positive phenotype, involves only subcutaneous tissues, and usually has an indolent
clinical course. The second group has a gamma/delta phenotype, is CD8 negative, often
co-expresses CD56, is not confined to the subcutaneous tissues, and usually has a
poor prognosis. In the recent WHO-EORTC classification, the term subcutaneous panniculitis-like
T-cell lymphoma is reserved for cases with an alpha/beta, CD8 positive phenotype.
Cases with a gamma/delta phenotype are included in the group of cutaneous gamma/delta
T-cell lymphomas.;
Neoplastic status : Malignant;
ICD-O code : 9708/3;
Codes from synonyms : C86.3;
Origin ID : C6918;
UMLS CUI : C0522624;
Currated CISMeF NLP mapping
Disease excludes abnormal cell
Disease excludes normal cell origin
Disease may have findings
Has associated anatomic sites
Semantic type(s)
UMLS correspondences (same concept)
concept_is_in_subset
disease_excludes_finding
disease_has_abnormal_cell
disease_has_finding
disease_has_molecular_abnormality
disease_has_normal_cell_origin
disease_has_normal_tissue_origin
disease_has_primary_anatomic_site
disease_may_have_abnormal_cell
disease_may_have_molecular_abnormality