Subcutaneous Panniculitis-Like T-Cell Lymphoma

Preferred Label : Subcutaneous Panniculitis-Like T-Cell Lymphoma;

NCIt synonyms : Subcutaneous Panniculitis-Like T-Cell Lymphoma (Alpha/Beta Type); Subcutaneous Panniculitis-Like T-Cell Lymphoma, Alpha/Beta Type; SPTCL;

NCIt definition : A cytotoxic primary cutaneous T-cell lymphoma. Recent studies suggest there are at least two groups of subcutaneous panniculitis-like T-cell lymphomas, each with distinct histologic features, immunophenotypic profile, and prognosis. One group has an alpha/beta, CD8 positive phenotype, involves only subcutaneous tissues, and usually has an indolent clinical course. The second group has a gamma/delta phenotype, is CD8 negative, often co-expresses CD56, is not confined to the subcutaneous tissues, and usually has a poor prognosis. In the recent WHO-EORTC classification, the term subcutaneous panniculitis-like T-cell lymphoma is reserved for cases with an alpha/beta, CD8 positive phenotype. Cases with a gamma/delta phenotype are included in the group of cutaneous gamma/delta T-cell lymphomas.;

Neoplastic status : Malignant;

ICD-O code : 9708/3;

Codes from synonyms : C86.3;

Details

Origin ID

C6918;

UMLS CUI

C0522624;

Currated CISMeF NLP mapping
- Subcutaneous panniculitic T-cell lymphoma (morphologic abnormality) [SNOMED CT concept]
- Subcutaneous panniculitic cutaneous T-cell lymphoma (disorder) [SNOMED CT concept]
- Subcutaneous panniculitis-like T-cell lymphoma [ICD-O code]
- Subcutaneous panniculitis-like T-cell lymphoma [ICD-10 Sub-category]
- Subcutaneous panniculitis-like T-cell lymphoma [ICD-11 Category]
- Subcutaneous panniculitis-like T-cell lymphoma [ICD-11 Category]
- Subcutaneous panniculitis-like T-cell lymphoma [MeSH concept]
- Subcutaneous panniculitis-like T-cell lymphoma [ORDO Disease]
- T-cell lymphoma, subcutaneous panniculitis-like [OMIM Phenotype]
- subcutaneous panniculitic T cell lymphoma [Disease (Nov.)]
- subcutaneous panniculitic t-cell lymphoma [SNOMED Notion]
- subcutaneous panniculitis-like T-cell lymphoma [MeSH Supplementary Concept]
Disease excludes abnormal cell
- Neoplastic B-Lymphocyte [NCIt concept]
- Reed-Sternberg Cell [NCIt concept]
Disease excludes normal cell origin
- Myeloid Cell [NCIt concept]
- Plasma Cell [NCIt concept]
- Precursor Natural Killer Cell [NCIt concept]
- Precursor T-Lymphoblast [NCIt concept]
Disease may have findings
- Fatigue [NCIt concept]
- Fever [NCIt concept]
- Karyorrhexis [NCIt concept]
- Necrotic Change [NCIt concept]
- Weight Loss [NCIt concept]
Excludes anatomical site(s)
- Lymph Node [NCIt concept]
Has associated anatomic sites
- Hematopoietic and Lymphatic System [NCIt concept]
- Integumentary System [NCIt concept]
- Skin [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Subcutaneous panniculitic T-cell lymphoma (morphologic abnormality) [SNOMED CT concept]
- Subcutaneous panniculitic cutaneous T-cell lymphoma (disorder) [SNOMED CT concept]
- Subcutaneous panniculitis-like T-cell lymphoma [MeSH concept]
- Subcutaneous panniculitis-like T-cell lymphoma [ICD-O code]
- Subcutaneous panniculitis-like T-cell lymphoma [ICD-10 Sub-category]
- Subcutaneous panniculitis-like T-cell lymphoma [ORDO Disease]
- Subcutaneous panniculitis-like T-cell lymphoma [ICD-11 Category]
- T-cell lymphoma, subcutaneous panniculitis-like [OMIM Phenotype]
- subcutaneous panniculitic T cell lymphoma [Disease (Nov.)]
- subcutaneous panniculitic t-cell lymphoma [SNOMED Notion]
- subcutaneous panniculitis-like T-cell lymphoma [MeSH Supplementary Concept]
concept_is_in_subset
- CTRP Disease Terminology [NCIt concept]
- CTRP Terminology [NCIt concept]
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology Terminology [NCIt concept]
- Mapped ICDO3.1 Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
- NCIt Neoplasm Core Terminology [NCIt concept]
- mCode Cancer Disorder Value Set [NCIt concept]
- mCode Elixhauser Lymphoma Value Set [NCIt concept]
- mCode Primary Cancer Disorder Value Set [NCIt concept]
- mCode Primary Malignant Neoplasm Disorder Value Set [NCIt concept]
- mCode Terminology [NCIt concept]
disease_excludes_finding
- Aggressive Clinical Course [NCIt concept]
- Benign Cellular Infiltrate [NCIt concept]
- CD4-Positive Neoplastic Cells Present [NCIt concept]
- CD56-Positive Neoplastic Cells Present [NCIt concept]
- Dermal Involvement [NCIt concept]
- Epidermotropic Lymphocytic Infiltrate [NCIt concept]
disease_has_abnormal_cell
- Abnormal Lymphocyte [NCIt concept]
- Malignant Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Hematopoietic and Lymphoid Cell [NCIt concept]
- Neoplastic Lymphocyte [NCIt concept]
- Neoplastic T-Lymphocyte [NCIt concept]
- Neoplastic T-Lymphocyte and Neoplastic Natural Killer Cell [NCIt concept]
disease_has_finding
- CD8-Positive Neoplastic Cells Present [NCIt concept]
- Cutaneous Involvement [NCIt concept]
- Extranodal Disease [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Rimming of Adipose Tissue Cells Present [NCIt concept]
- Subcutaneous Involvement [NCIt concept]
- Subcutaneous Nodule [NCIt concept]
disease_has_molecular_abnormality
- Clonal T-Cell Receptor Beta Chain Gene Rearrangement [NCIt concept]
- Clonal T-Cell Receptor Gamma Chain Gene Rearrangement [NCIt concept]
disease_has_normal_cell_origin
- Cytotoxic T-Lymphocyte [NCIt concept]
- Hematopoietic and Lymphoid Cell [NCIt concept]
- Lymphocyte [NCIt concept]
- Peripheral (Post-Thymic) T-Lymphocyte [NCIt concept]
- Peripheral (Post-Thymic) T-Lymphocyte and Natural Killer Cell [NCIt concept]
- T-Lymphocyte and Natural Killer Cell [NCIt concept]
disease_has_normal_tissue_origin
- Hematopoietic and Lymphoid Tissue [NCIt concept]
- Lymphoid Tissue [NCIt concept]
- Subcutis [NCIt concept]
disease_has_primary_anatomic_site
- Hematopoietic and Lymphatic System [NCIt concept]
- Lymphatic System [NCIt concept]
- Skin [NCIt concept]
disease_may_have_abnormal_cell
- Neoplastic Large T-Lymphocyte [NCIt concept]
- Neoplastic Medium-Sized T-Lymphocyte [NCIt concept]
- Neoplastic Small T-Lymphocyte [NCIt concept]
disease_may_have_molecular_abnormality
- Germline HAVCR2 Gene Mutation [NCIt concept]

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