Malignant Pancreatic Vipoma

Preferred Label : Malignant Pancreatic Vipoma;

NCIt definition : A pancreatic neuroendocrine tumor producing vasoactive intestinal peptide (VIP). It is associated with watery diarrhea, hypokalemia, and hypochlorhydria or achlorhydria. It displays vascular invasion and metastasizes to other anatomic sites. One third of cases are metastatic at the time of diagnosis.;

Neoplastic status : Malignant;

Details

Origin ID

C67461;

UMLS CUI

C1881586;

Disease excludes abnormal cell
- Large Osteoclastic Giant Cell [NCIt concept]
- Neoplastic Smooth Muscle Cell [NCIt concept]
Has associated anatomic sites
- Digestive System [NCIt concept]
- Pancreas [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
disease_excludes_finding
- Absence of a Hormonal Syndrome [NCIt concept]
- High Mitotic Activity [NCIt concept]
- Low Grade Neuroendocrine Lesion [NCIt concept]
- Poorly Differentiated Neuroendocrine Lesion [NCIt concept]
- Severe Cytologic Atypia [NCIt concept]
disease_has_abnormal_cell
- Neoplastic Cell [NCIt concept]
- Neoplastic Endocrine Cell [NCIt concept]
- Neoplastic Epithelial Cell [NCIt concept]
- Neoplastic Neuroendocrine Cell [NCIt concept]
disease_has_associated_disease
- WDHA Syndrome [NCIt concept]
disease_has_finding
- Diarrhea [NCIt concept]
- Endocrine Differentiation [NCIt concept]
- Epithelial Component Present [NCIt concept]
- Hypokalemia [NCIt concept]
- Intermediate Grade Neuroendocrine Lesion [NCIt concept]
- Low Mitotic Activity [NCIt concept]
- Neuroendocrine Differentiation [NCIt concept]
- Presence of a Hormonal Syndrome [NCIt concept]
- Tumor Vascular Invasion [NCIt concept]
- VIP-Positive Neoplastic Cells Present [NCIt concept]
- Well Differentiated Neuroendocrine Lesion [NCIt concept]
disease_has_normal_cell_origin
- Endocrine Cell of the Digestive System [NCIt concept]
- Epithelial Cell [NCIt concept]
- Islet Cell [NCIt concept]
disease_has_normal_tissue_origin
- Epithelial Tissue [NCIt concept]
- Islet of Langerhans [NCIt concept]
disease_has_primary_anatomic_site
- Digestive System [NCIt concept]
- Islet of Langerhans [NCIt concept]
- Pancreas [NCIt concept]
disease_mapped_to_gene
- MEN1 Gene [NCIt concept]
- VHL Gene [NCIt concept]
disease_may_have_associated_disease
- Multiple Endocrine Neoplasia Type 1 [NCIt concept]

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