Cardiac Undifferentiated Pleomorphic Sarcoma

Preferred Label : Cardiac Undifferentiated Pleomorphic Sarcoma;

NCIt synonyms : Cardiac Unclassified Pleomorphic Sarcoma (Formerly Cardiac MFH); Cardiac Malignant Fibrous Histiocytoma; Heart Undifferentiated Pleomorphic Sarcoma; Cardiac Unclassified Pleomorphic Sarcoma (Formerly Cardiac Malignant Fibrous Histiocytoma); Cardiac Unclassified Pleomorphic Sarcoma;

NCIt definition : An undifferentiated pleomorphic sarcoma usually arising from the left atrium of the heart. It is characterized by the presence of fibrohistiocytic cells, giant cells, and spindle cells arrranged iin a storiform pattern. Clinical presentation includes signs and symptoms associated with left atrial hemodynamic changes.;

Neoplastic status : Malignant;

Details

Origin ID

C45755;

UMLS CUI

C1704615;

Disease excludes normal cell origin
- Epithelial Cell [NCIt concept]
Excludes anatomical site(s)
- Bone [NCIt concept]
- Neck [NCIt concept]
- Pericardial Cavity [NCIt concept]
Has associated anatomic sites
- Cardiovascular System [NCIt concept]
- Connective and Soft Tissue [NCIt concept]
- Heart [NCIt concept]
- Respiratory System [NCIt concept]
- Thoracic Cavity [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Indolent Clinical Course [NCIt concept]
- Intermediate Filaments Present [NCIt concept]
- Intracytoplasmic Eosinophilic Inclusion [NCIt concept]
disease_excludes_normal_tissue_origin
- Epithelial Tissue [NCIt concept]
disease_has_abnormal_cell
- Giant Cell [NCIt concept]
- Malignant Cell [NCIt concept]
- Malignant Spindle-Shaped Fibrohistiocytic Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Primitive Mesenchymal Cell [NCIt concept]
disease_has_finding
- Cellular Pleomorphism [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- No Identifiable Line of Differentiation [NCIt concept]
- Storiform Growth Pattern [NCIt concept]
disease_has_normal_tissue_origin
- Connective and Soft Tissue [NCIt concept]
- Soft Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Heart [NCIt concept]
disease_may_have_cytogenetic_abnormality
- Double Minutes [NCIt concept]
- Gain of Chromosome 19 [NCIt concept]
- Gain of Chromosome 1p31 [NCIt concept]
- Gain of Chromosome 7p [NCIt concept]
- Gain of Chromosome 7q32 [NCIt concept]
- Loss of Chromosome 11 [NCIt concept]
- Loss of Chromosome 13 [NCIt concept]
- Loss of Chromosome 16 [NCIt concept]
- Loss of Chromosome 2p [NCIt concept]
- Loss of Chromosome 2q [NCIt concept]
- Supernumerary Circular Chromosome [NCIt concept]

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