Primary Cutaneous CD8-Positive Aggressive Epidermotropic Cytotoxic T-Cell Lymphoma

Preferred Label : Primary Cutaneous CD8-Positive Aggressive Epidermotropic Cytotoxic T-Cell Lymphoma;

NCIt synonyms : Primary Cutaneous Aggressive Epidermotropic CD8-Positive T-Cell Lymphoma; Primary Cutaneous CD8-Positive Aggressive Epidermotropic T-Cell Lymphoma; PCAETL;

NCIt definition : An aggressive, epidermotropic primary cutaneous T-cell lymphoma composed of small to medium-sized, or medium-sized to large, CD8-positive T-lymphocytes with pleomorphic or blastic nuclei. Epidermotropism is often pronounced, and angiocentricity and angioinvasion may be present. It manifests with localized or disseminated eruptive papules and nodules or tumors.;

Neoplastic status : Malignant;

ICD-O code : 9709/3;

Details

Origin ID

C45339;

UMLS CUI

C4518232;

Automatic exact mappings (from CISMeF team)
- Primary cutaneous CD8-positive aggressive epidermotropic cytotoxic T-cell lymphoma [ICD-11 More detail]
Disease excludes abnormal cell
- Lymphocyte Predominant Cell [NCIt concept]
- Neoplastic B-Lymphocyte [NCIt concept]
- Reed-Sternberg Cell [NCIt concept]
Disease excludes normal cell origin
- Myeloid Cell [NCIt concept]
- Plasma Cell [NCIt concept]
- Precursor Natural Killer Cell [NCIt concept]
- Precursor T-Lymphoblast [NCIt concept]
Disease may have findings
- Aggressive Clinical Course [NCIt concept]
- Angiocentric Pattern [NCIt concept]
- Angioinvasion [NCIt concept]
- Extracutaneous Dissemination of Disease [NCIt concept]
- Localized Skin Lesion [NCIt concept]
- Multiple Tumor Masses [NCIt concept]
- Necrotic Lesion [NCIt concept]
- Papular Lesion [NCIt concept]
- Skin Nodule [NCIt concept]
- Skin Patch [NCIt concept]
- Skin Plaque [NCIt concept]
Excludes anatomical site(s)
- Lymph Node [NCIt concept]
Has associated anatomic sites
- Hematopoietic and Lymphatic System [NCIt concept]
- Integumentary System [NCIt concept]
- Skin [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Primary cutaneous CD8 positive aggressive epidermotropic cytotoxic T-cell lymphoma (disorder) [SNOMED CT concept]
- Primary cutaneous CD8 positive aggressive epidermotropic cytotoxic T-cell lymphoma (morphologic abnormality) [SNOMED CT concept]
concept_is_in_subset
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- NCIt Neoplasm Core Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- CD30-Positive Neoplastic Cells Present [NCIt concept]
disease_has_abnormal_cell
- Abnormal Lymphocyte [NCIt concept]
- Malignant Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Hematopoietic and Lymphoid Cell [NCIt concept]
- Neoplastic Lymphocyte [NCIt concept]
- Neoplastic T-Lymphocyte [NCIt concept]
- Neoplastic T-Lymphocyte and Neoplastic Natural Killer Cell [NCIt concept]
disease_has_finding
- CD8-Positive Neoplastic Cells Present [NCIt concept]
- Cutaneous Involvement [NCIt concept]
- Epidermotropic Lymphocytic Infiltrate [NCIt concept]
- Extranodal Disease [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Nuclear Pleomorphism [NCIt concept]
disease_has_molecular_abnormality
- Clonal T-Cell Receptor Beta Chain Gene Rearrangement [NCIt concept]
- Clonal T-Cell Receptor Gamma Chain Gene Rearrangement [NCIt concept]
disease_has_normal_cell_origin
- Cytotoxic T-Lymphocyte [NCIt concept]
- Hematopoietic and Lymphoid Cell [NCIt concept]
- Lymphocyte [NCIt concept]
- Peripheral (Post-Thymic) T-Lymphocyte [NCIt concept]
- Peripheral (Post-Thymic) T-Lymphocyte and Natural Killer Cell [NCIt concept]
- T-Lymphocyte and Natural Killer Cell [NCIt concept]
disease_has_normal_tissue_origin
- Hematopoietic and Lymphoid Tissue [NCIt concept]
- Lymphoid Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Hematopoietic and Lymphatic System [NCIt concept]
- Lymphatic System [NCIt concept]
- Skin [NCIt concept]
disease_may_have_abnormal_cell
- Neoplastic Medium-Sized to Large T-Lymphocyte [NCIt concept]
- Neoplastic Small to Medium-Sized T-Lymphocyte [NCIt concept]

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