Pancreatoblastoma

Preferred Label : Pancreatoblastoma;

NCIt definition : A rare malignant epithelial neoplasm arising from the pancreas. The vast majority of cases occur during childhood. It is characterized by acinar differentiation, the formation of squamoid corpuscles, and the formation of stromal bands. Patients may present with an abdominal mass. Symptoms include pain, weight loss, and diarrhea. It may metastasize to lymph nodes, liver, and distant anatomic sites. Children who do not have metastatic disease at the time of diagnosis usually have a favorable clinical outcome when treated with a combination of surgery and chemotherapy. However, children with metastatic disease at presentation or adult patients usually have a poor prognosis.;

Neoplastic status : Malignant;

ICD-O code : 8971/3;

Details

Origin ID

C4265;

UMLS CUI

C0334489;

Automatic exact mappings (from CISMeF team)
- Pancreatoblastoma [MedDRA Preferred Term]
- Pancreatoblastoma [ICD-11 Extension code]
- Pancreatoblastoma [ICD-11 Extension code]
- Pancreatoblastoma [HRDO Sign]
- Pancreatoblastoma (disorder) [SNOMED CT concept]
- pancreatoblastoma [DO Concept]
- pancreatoblastoma [Radlex concept]
Currated CISMeF NLP mapping
- Pancreatoblastoma [HPO term]
- Pancreatoblastoma [MeSH concept]
- Pancreatoblastoma [ICD-O code]
- Pancreatoblastoma [ORDO Disease]
- Pancreatoblastoma (morphologic abnormality) [SNOMED CT concept]
- pancreatoblastoma [MeSH Supplementary Concept]
- pancreatoblastoma [SNOMED Notion]
DO Cross reference
- pancreatoblastoma [DO Concept]
Disease may have findings
- Abdominal Pain [NCIt concept]
- Jaundice [NCIt concept]
- Pruritus [NCIt concept]
- Weight Loss [NCIt concept]
Has associated anatomic sites
- Digestive System [NCIt concept]
- Pancreas [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Pancreatoblastoma [MedDRA Preferred Term]
- Pancreatoblastoma [ORDO Disease]
- Pancreatoblastoma [MeSH concept]
- Pancreatoblastoma [ICD-O code]
- Pancreatoblastoma [HPO term]
- Pancreatoblastoma (disorder) [SNOMED CT concept]
- Pancreatoblastoma (morphologic abnormality) [SNOMED CT concept]
- pancreatoblastoma [MeSH Supplementary Concept]
- pancreatoblastoma [DO Concept]
- pancreatoblastoma [SNOMED Notion]
concept_is_in_subset
- Cellosaurus Disease Terminology [NCIt concept]
- Cellosaurus Terminology [NCIt concept]
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology Terminology [NCIt concept]
- Mapped ICDO3.1 Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
disease_has_abnormal_cell
- Malignant Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
disease_has_finding
- Acinar Pattern [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Squamoid Corpuscle [NCIt concept]
disease_has_primary_anatomic_site
- Exocrine Pancreas [NCIt concept]
disease_may_have_associated_disease
- Beckwith-Wiedemann Syndrome [NCIt concept]

Keyword's position in hierarchy(ies) :

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