" /> Pancreatoblastoma - CISMeF





ICD-11 code : XH27L5;

Preferred Label : Pancreatoblastoma;

ICD-11 definition : Pancreatoblastoma is a very rare malignant epithelial neoplasm of the pancreas showing multiple lines of differentiation including acinar differentiation and squamoid nests. Endocrine and ductal differentiation, and a distinct mesenchymal component, can also be seen. Most pancreatoblastomas occur in children. Pancreatoblastoma is the most common malignant pancreatic neoplasm of childhood. It has been reported in newborns with Beckwith-Wiedemann syndrome. Grossly, pancreatoblastomas are usually large and well-demarcated, and are often palpable in children. They are fully malignant neoplasms.;

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Pancreatoblastoma is a very rare malignant epithelial neoplasm of the pancreas showing multiple lines of differentiation including acinar differentiation and squamoid nests. Endocrine and ductal differentiation, and a distinct mesenchymal component, can also be seen. Most pancreatoblastomas occur in children. Pancreatoblastoma is the most common malignant pancreatic neoplasm of childhood. It has been reported in newborns with Beckwith-Wiedemann syndrome. Grossly, pancreatoblastomas are usually large and well-demarcated, and are often palpable in children. They are fully malignant neoplasms.

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27/07/2025


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