Plexiform Neurofibroma

Preferred Label : Plexiform Neurofibroma;

NCIt definition : An elongated and multinodular neurofibroma, formed when the tumor involves either multiple trunks of a plexus or multiple fascicles of a large nerve, such as the sciatic. Some plexiform neurofibromas resemble a bag of worms, others produce a massive ropy enlargement of the nerve. (Adapted from WHO);

Alternative definition : NCI-GLOSS: A nerve that has become thick and misshapen due to the abnormal growth of cells and tissues that cover the nerve.;

Neoplastic status : Benign;

ICD-O code : 9550/0;

Codes from synonyms : 10065866; CDR0000045094;

Details

Origin ID

C3797;

UMLS CUI

C0206728;

Automatic exact mappings (from CISMeF team)
- Plexiform neurofibroma [ICD-9 code]
- Plexiform neurofibroma [ICD-11 Extension code]
Currated CISMeF NLP mapping
- Plexiform neurofibroma [HPO term]
- Plexiform neurofibroma [ICD-O code]
- Plexiform neurofibroma [MedDRA LLT]
- Plexiform neurofibroma (disorder) [SNOMED CT concept]
- Plexiform neurofibroma (morphologic abnormality) [SNOMED CT concept]
- neurofibroma, plexiform [MeSH Descriptor]
- neurofibroma, plexiform [MeSH concept]
- plexiform neurofibroma [DO Concept]
- plexiform neurofibroma [Disease (Nov.)]
- plexiform neurofibroma [SNOMED Notion]
- plexiform neurofibroma [Radlex concept]
DO Cross reference
- plexiform neurofibroma [DO Concept]
Disease excludes abnormal cell
- Malignant Cell [NCIt concept]
Has associated anatomic sites
- Nervous System [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Plexiform neurofibroma [MedDRA LLT]
- Plexiform neurofibroma [ICD-O code]
- Plexiform neurofibroma [HPO term]
- Plexiform neurofibroma (disorder) [SNOMED CT concept]
- Plexiform neurofibroma (morphologic abnormality) [SNOMED CT concept]
- neurofibroma, plexiform [MeSH concept]
- neurofibroma, plexiform [MeSH Descriptor]
- plexiform neurofibroma [Radlex concept]
- plexiform neurofibroma [DO Concept]
- plexiform neurofibroma [Disease (Nov.)]
- plexiform neurofibroma [SNOMED Notion]
concept_is_in_subset
- CTRP Disease Terminology [NCIt concept]
- CTRP Terminology [NCIt concept]
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology Terminology [NCIt concept]
- Mapped ICDO3.1 Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
- NCI CTEP SDC Non-Rhabdomyosarcoma Soft Tissue Sarcoma Sub-Category Terminology [NCIt concept]
- NCI CTEP Simplified Disease Classification Terminology [NCIt concept]
disease_excludes_finding
- Encapsulated Mass [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
disease_has_abnormal_cell
- Neoplastic Cell [NCIt concept]
- Neoplastic Fibroblast-Like Cell [NCIt concept]
- Neoplastic Neuroepithelial Cell and Neoplastic Perineural Cell [NCIt concept]
- Neoplastic Perineural Cell [NCIt concept]
- Neoplastic Perineurial-Like Cell [NCIt concept]
- Neoplastic Schwann Cell [NCIt concept]
disease_has_associated_disease
- Neurofibromatosis Type 1 with Inoperable, Progressive, Symptomatic Plexiform Neurofibromas [NCIt concept]
disease_has_finding
- Benign Cellular Infiltrate [NCIt concept]
- Multinodular Lesion [NCIt concept]
- Plexiform Growth Pattern [NCIt concept]
disease_has_grade
- Grade 1 [NCIt concept]
disease_has_normal_cell_origin
- Neuron, Neuroepithelial Cell, and Supporting Cell of the Nervous System [NCIt concept]
- Perineural Cell [NCIt concept]
disease_has_normal_tissue_origin
- Nerve Tissue and Nerve Sheaths [NCIt concept]
- Nerve Tissue, Neuroepithelial Tissue, and Nerve Sheaths [NCIt concept]
disease_has_primary_anatomic_site
- Nervous System [NCIt concept]
- Peripheral Nerve [NCIt concept]
disease_mapped_to_gene
- NF1 Gene [NCIt concept]
disease_may_have_molecular_abnormality
- NF1 Gene Inactivation [NCIt concept]

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