Preferred Label : neurofibroma, plexiform;
MeSH definition : A type of neurofibroma manifesting as a diffuse overgrowth of subcutaneous tissue,
usually involving the face, scalp, neck, and chest but occasionally occurring in the
abdomen or pelvis. The tumors tend to progress, and may extend along nerve roots to
eventually involve the spinal roots and spinal cord. This process is almost always
a manifestation of NEUROFIBROMATOSIS 1. (From Adams et al., Principles of Neurology,
6th ed, p1016; J Pediatr 1997 Nov;131(5):678-82);
MeSH synonym : elephantiasis neuromatoses; elephantiasis neuromatosis; neuromas, plexiform; pachydermatocele; pachydermatoceles; plexiform neurofibroma; plexiform neurofibromas; plexiform neuromas; tumor royale; neuroma, plexiform; plexiform neuroma; neurofibromas, plexiform;
MeSH annotation : coord IM with precoord organ/neopl term (IM);
Origin ID : D018318;
UMLS CUI : C0206728;
Allowable qualifiers
- Automatic exact mappings (from CISMeF team)
- Currated CISMeF NLP mapping
- DO Cross reference
- HPO term
- Record concept(s)
- See also inter- (CISMeF)
- Semantic type(s)
- UMLS correspondences (same concept)
A type of neurofibroma manifesting as a diffuse overgrowth of subcutaneous tissue,
usually involving the face, scalp, neck, and chest but occasionally occurring in the
abdomen or pelvis. The tumors tend to progress, and may extend along nerve roots to
eventually involve the spinal roots and spinal cord. This process is almost always
a manifestation of NEUROFIBROMATOSIS 1. (From Adams et al., Principles of Neurology,
6th ed, p1016; J Pediatr 1997 Nov;131(5):678-82)
