Epithelioid Sarcoma

Preferred Label : Epithelioid Sarcoma;

NCIt synonyms : Epithelioid Cell Sarcoma; ES;

NCIt definition : An aggressive malignant neoplasm of uncertain differentiation, characterized by the presence of epithelioid cells forming nodular patterns. The nodules often undergo central necrosis, resulting in a pseudogranulomatous growth pattern. It usually occurs in young adults. The most common sites of involvement are the extremities (distal-type epithelioid sarcoma), and less frequently the pelvis, perineum, and genital organs (proximal-type epithelioid sarcoma).;

Neoplastic status : Malignant;

ICD-O code : 8804/3;

Details

Origin ID

C3714;

UMLS CUI

C0205944;

Automatic exact mappings (from CISMeF team)
- Epithelioid cell sarcoma [ICD-9 code]
- Epithelioid sarcoma [ICD-11 Extension code]
- Epithelioid sarcoma (disorder) [SNOMED CT concept]
- Ewing sarcoma [OMIM Phenotype]
- ethics [MeSH Descriptor]
Currated CISMeF NLP mapping
- Epithelioid sarcoma [PASCAL descriptor]
- Epithelioid sarcoma [MedDRA Preferred Term]
- Epithelioid sarcoma [ICD-O code]
- Epithelioid sarcoma [ORDO Disease]
- Epithelioid sarcoma (morphologic abnormality) [SNOMED CT concept]
- Epithelioid sarcoma NOS [MedDRA LLT]
- Epithelioid sarcomas [MedDRA High Level Term]
- epithelioid sarcoma [DO Concept]
- epithelioid sarcoma [Disease (Nov.)]
- epithelioid sarcoma [SNOMED Notion]
- sarcoma [MeSH Descriptor]
- sarcoma, epithelioid [MeSH concept]
DO Cross reference
- epithelioid sarcoma [DO Concept]
Disease excludes normal cell origin
- Epithelial Cell [NCIt concept]
Disease may have findings
- Aggressive Clinical Course [NCIt concept]
- Loss of INI 1 Protein Expression [NCIt concept]
- Necrotic Change [NCIt concept]
Excludes anatomical site(s)
- Bone [NCIt concept]
Has associated anatomic sites
- Connective and Soft Tissue [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Epithelioid sarcoma [ICD-O code]
- Epithelioid sarcoma [ORDO Disease]
- Epithelioid sarcoma [MedDRA Preferred Term]
- Epithelioid sarcoma (disorder) [SNOMED CT concept]
- Epithelioid sarcoma (morphologic abnormality) [SNOMED CT concept]
- Epithelioid sarcoma NOS [MedDRA LLT]
- Epithelioid sarcomas [MedDRA High Level Term]
- epithelioid sarcoma [DO Concept]
- epithelioid sarcoma [Disease (Nov.)]
- epithelioid sarcoma [SNOMED Notion]
- sarcoma, epithelioid [MeSH concept]
concept_is_in_subset
- CPTAC Baseline Medical Forms Terminology [NCIt concept]
- CPTAC Sarcoma Baseline Form [NCIt concept]
- CPTAC Terminology [NCIt concept]
- CTRP Disease Terminology [NCIt concept]
- CTRP Terminology [NCIt concept]
- Cellosaurus Disease Terminology [NCIt concept]
- Cellosaurus Terminology [NCIt concept]
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology Terminology [NCIt concept]
- Mapped ICDO3.1 Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Indolent Clinical Course [NCIt concept]
- Intermediate Filaments Present [NCIt concept]
- Intracytoplasmic Eosinophilic Inclusion [NCIt concept]
disease_excludes_normal_tissue_origin
- Epithelial Tissue [NCIt concept]
disease_has_abnormal_cell
- Malignant Cell [NCIt concept]
- Malignant Epithelioid Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
disease_has_finding
- Malignant Cellular Infiltrate [NCIt concept]
- Metastatic/Recurrent Disease [NCIt concept]
- Tissue Differentiation Uncertain [NCIt concept]
disease_has_normal_tissue_origin
- Connective and Soft Tissue [NCIt concept]
- Soft Tissue [NCIt concept]
disease_may_have_cytogenetic_abnormality
- Gain of Chromosome 11q13 [NCIt concept]
- Loss of Chromosome 22q [NCIt concept]
- Loss of Chromosome 8p [NCIt concept]
- i(8)(q10) [NCIt concept]

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