Folliculotropic Mycosis Fungoides

Preferred Label : Folliculotropic Mycosis Fungoides;

NCIt synonyms : Follicular Mycosis Fungoides; Mycosis Fungoides-Associated Follicular Mucinosis;

NCIt definition : A rare variant of mycosis fungoides, characterized by cerebriform lymphocytic infiltration of the hair follicles of the head and neck. Most cases show mucinous degeneration of the hair follicles, and are designated as mycosis fungoides-associated follicular mucinosis. Cases without mucinous degeneration have been reported as pilotropic mycosis fungoides. There is no difference in clinical presentation or outcome between mycosis fungoides-associated follicular mucinosis and pilotropic mycosis fungoides. In the recent WHO-EORTC classification, folliculotropic mycosis fungoides is the preferred term for all cases.;

Neoplastic status : Malignant;

Details

Origin ID

C35685;

UMLS CUI

C1627767;

Automatic exact mappings (from CISMeF team)
- Follicular mucinosis type mycosis fungoides (disorder) [SNOMED CT concept]
- Folliculotropic mycosis fungoides [ICD-11 More detail]
Currated CISMeF NLP mapping
- Folliculotropic mycosis fungoides [ORDO Disease]
Disease excludes abnormal cell
- Neoplastic B-Lymphocyte [NCIt concept]
- Reed-Sternberg Cell [NCIt concept]
Disease excludes normal cell origin
- Myeloid Cell [NCIt concept]
- Plasma Cell [NCIt concept]
- Precursor Natural Killer Cell [NCIt concept]
- Precursor T-Lymphoblast [NCIt concept]
Disease may have findings
- Mucinous Degeneration [NCIt concept]
Excludes anatomical site(s)
- Lymph Node [NCIt concept]
False automatic mappings
- Follicular mycosis fungoides (morphologic abnormality) [SNOMED CT concept]
Has associated anatomic sites
- Head and Neck [NCIt concept]
- Hematopoietic and Lymphatic System [NCIt concept]
- Integumentary System [NCIt concept]
- Skin [NCIt concept]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
UMLS correspondences (same concept)
- Follicular mucinosis type mycosis fungoides (disorder) [SNOMED CT concept]
- Follicular mycosis fungoides (morphologic abnormality) [SNOMED CT concept]
- Folliculotropic mycosis fungoides [ORDO Disease]
disease_excludes_finding
- Aggressive Clinical Course [NCIt concept]
- Benign Cellular Infiltrate [NCIt concept]
- Epidermotropic Lymphocytic Infiltrate [NCIt concept]
disease_has_abnormal_cell
- Abnormal Lymphocyte [NCIt concept]
- Cerebriform Lymphocyte [NCIt concept]
- Malignant Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Hematopoietic and Lymphoid Cell [NCIt concept]
- Neoplastic Lymphocyte [NCIt concept]
- Neoplastic T-Lymphocyte [NCIt concept]
- Neoplastic T-Lymphocyte and Neoplastic Natural Killer Cell [NCIt concept]
disease_has_associated_disease
- Mycosis Fungoides [NCIt concept]
disease_has_finding
- Cutaneous Involvement [NCIt concept]
- Extranodal Disease [NCIt concept]
- Folliculotropic Lymphocytic Infiltrate [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
disease_has_normal_cell_origin
- Hematopoietic and Lymphoid Cell [NCIt concept]
- Lymphocyte [NCIt concept]
- Peripheral (Post-Thymic) T-Lymphocyte [NCIt concept]
- Peripheral (Post-Thymic) T-Lymphocyte and Natural Killer Cell [NCIt concept]
- Peripheral Epidermotropic T-Lymphocyte [NCIt concept]
- T-Lymphocyte and Natural Killer Cell [NCIt concept]
disease_has_normal_tissue_origin
- Hematopoietic and Lymphoid Tissue [NCIt concept]
- Lymphoid Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Hematopoietic and Lymphatic System [NCIt concept]
- Lymphatic System [NCIt concept]
- Skin [NCIt concept]
disease_may_have_associated_disease
- Alopecia Mucinosa [NCIt concept]
disease_may_have_molecular_abnormality
- Clonal T-Cell Receptor Beta Chain Gene Rearrangement [NCIt concept]
- Clonal T-Cell Receptor Gamma Chain Gene Rearrangement [NCIt concept]

Keyword's position in hierarchy(ies) :

You can consult :

recommendations
documents concerning education
documents for patients