Granulomatous Slack Skin Disease

Preferred Label : Granulomatous Slack Skin Disease;

NCIt definition : A rare variant of mycosis fungoides, characterized by the development of folds of lax skin in the axillae or groins. It has been reported in association with Hodgkin lymphoma. Morphologically, there is a dense granulomatous dermal atypical lymphocytic infiltrate, often associated with multinucleated giant cells. Destruction of elastic tissue is present. Most cases have an indolent clinical course.;

Neoplastic status : Malignant;

Details

Origin ID

C35464;

UMLS CUI

C0457002;

Automatic exact mappings (from CISMeF team)
- lymphoma, T-cell, cutaneous [MeSH Descriptor]
Currated CISMeF NLP mapping
- Granulomatous slack skin [ORDO Disease]
- Granulomatous slack skin [PASCAL descriptor]
- Granulomatous slack skin [ICD-11 More detail]
- Granulomatous slack skin [ICD-11 Extension code]
- Granulomatous slack skin disease (disorder) [SNOMED CT concept]
- granulomatous slack skin [MeSH concept]
Disease excludes abnormal cell
- Lymphocyte Predominant Cell [NCIt concept]
- Neoplastic B-Lymphocyte [NCIt concept]
- Reed-Sternberg Cell [NCIt concept]
Disease excludes normal cell origin
- Myeloid Cell [NCIt concept]
- Plasma Cell [NCIt concept]
- Precursor Natural Killer Cell [NCIt concept]
- Precursor T-Lymphoblast [NCIt concept]
Disease may have findings
- Chronic Clinical Course [NCIt concept]
- Dermatopathic Lymphadenopathy [NCIt concept]
- Pautrier Microabscess Present [NCIt concept]
- Progressive Disease [NCIt concept]
- Scaly Skin Eruption [NCIt concept]
- Single Cell Exocytosis [NCIt concept]
- Skin Patch [NCIt concept]
- Skin Plaque [NCIt concept]
Excludes anatomical site(s)
- Lymph Node [NCIt concept]
Has associated anatomic sites
- Hematopoietic and Lymphatic System [NCIt concept]
- Integumentary System [NCIt concept]
- Skin [NCIt concept]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
UMLS correspondences (same concept)
- Granulomatous slack skin [ORDO Disease]
- Granulomatous slack skin disease (disorder) [SNOMED CT concept]
disease_excludes_finding
- Aggressive Clinical Course [NCIt concept]
- Benign Cellular Infiltrate [NCIt concept]
disease_has_abnormal_cell
- Abnormal Lymphocyte [NCIt concept]
- Cerebriform Lymphocyte [NCIt concept]
- Malignant Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Hematopoietic and Lymphoid Cell [NCIt concept]
- Neoplastic Lymphocyte [NCIt concept]
- Neoplastic T-Lymphocyte [NCIt concept]
- Neoplastic T-Lymphocyte and Neoplastic Natural Killer Cell [NCIt concept]
disease_has_associated_disease
- Skin Atrophy [NCIt concept]
disease_has_finding
- Cutaneous Involvement [NCIt concept]
- Elastophagocytosis [NCIt concept]
- Epidermotropic Lymphocytic Infiltrate [NCIt concept]
- Extranodal Disease [NCIt concept]
- Granuloma [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Rare Lesion [NCIt concept]
disease_has_normal_cell_origin
- Hematopoietic and Lymphoid Cell [NCIt concept]
- Lymphocyte [NCIt concept]
- Peripheral (Post-Thymic) T-Lymphocyte [NCIt concept]
- Peripheral (Post-Thymic) T-Lymphocyte and Natural Killer Cell [NCIt concept]
- Peripheral Epidermotropic T-Lymphocyte [NCIt concept]
- T-Lymphocyte and Natural Killer Cell [NCIt concept]
disease_has_normal_tissue_origin
- Hematopoietic and Lymphoid Tissue [NCIt concept]
- Lymphoid Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Hematopoietic and Lymphatic System [NCIt concept]
- Lymphatic System [NCIt concept]
- Skin [NCIt concept]
disease_may_have_associated_disease
- Hodgkin Lymphoma [NCIt concept]
disease_may_have_molecular_abnormality
- CDKN2A Gene Inactivation [NCIt concept]
- Clonal T-Cell Receptor Beta Chain Gene Rearrangement [NCIt concept]
- Clonal T-Cell Receptor Gamma Chain Gene Rearrangement [NCIt concept]
- PTEN Gene Inactivation [NCIt concept]

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