Preferred Label : Kawasaki Disease;
NCIt synonyms : Mucocutaneous Lymph Node Syndrome;
NCIt related terms : Infantile Polyarteritis Nodosa; Mucocutaneous lymph node syndrome [Kawasaki];
NCIt definition : A vasculitis characterized by inflammation of the arteries, particularly the coronary
arteries. The vasculitis may lead to aneurysm formation and possibly, heart attacks.
It affects young children who usually present with persistent high fever, redness
of the mucous membranes of the mouth, redness of the palms and soles, skin rashes,
lymphadenitis, and joint pain and swelling.;
Alternative definition : NICHD: Medium-sized vessel vasculitis seen primarily in young children with predilection
for the coronary arteries. Diagnosis is based on clinical findings of persistent high
fever, changes in lips and oral mucous membranes, erythema and edema of hands/feet
and later desquamation, bilateral bulbar conjunctivitis, unilateral cervical adenopathy,
polymorphous rash.; ACC/AHA: Kawasaki disease is an acute self-limited vasculitis of childhood that is
characterized by fever, bilateral nonexudative conjunctivitis, erythema of the lips
and oral mucosa, changes in the extremities, rash, and cervical lymphadenopathy.;
Codes from synonyms : M30.3;
Origin ID : C34825;
UMLS CUI : C0026691;
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
DO Cross reference
Has associated anatomic sites
Semantic type(s)
UMLS correspondences (same concept)
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