Mucocutaneous lymph node syndrome

ICD-11 code : 4A44.5;

Preferred Label : Mucocutaneous lymph node syndrome;

ICD-11 definition : Mucocutaneous lymph node syndrome (Kawasaki disease) is a globally distributed acute vasculitis of young children affecting medium to small calibre arteries and if untreated leads to coronary artery aneurysms in about a quarter of cases. Cardinal signs include cervical lymphadenopathy, conjunctival injection, rash (maculopapular, erythrodermic or erythema multiforme-like), strawberry tongue, oropharyngeal erythema, erythema and swelling of hands and feet and periungual desquamation. The cause is unknown but thought to be environmental, possibly from viral infection. A variant of the disease has been linked to SARS CoV-2 infection.;

ICD-11 synonym : Kawasaki syndrome; Kawasaki disease; Acute febrile mucocutaneous lymph node syndrome;

ICD-11 inclusion : Kawasaki syndrome;

Details

Origin ID

540285662;

UMLS CUI

C0026691;

Automatic exact mappings (from CISMeF team)
- Kawasaki disease [DO Concept]
Currated CISMeF NLP mapping
- Acute febrile mucocutaneous lymph node syndrome (disorder) [SNOMED CT concept]
- Kawasaki Disease [NCIt concept]
- Kawasaki disease [ORDO Disease]
- Kawasaki disease [OMIM Phenotype]
- Kawasaki disease [Radlex concept]
- Kawasaki disease [COVID-19 Thesaurus concept]
- Kawasaki syndrome [PASCAL descriptor]
- Kawasaki's disease [MedDRA Preferred Term]
- Mucocutaneous lymph node syndrome [MedDRA LLT]
- acute febrile mucocutaneous lymph node syndrome [SNOMED Notion]
- kawasaki disease [MedlinePlus Topic]
- mucocutaneous lymph node syndrome [MeSH concept]
- mucocutaneous lymph node syndrome [MeSH Descriptor]
ICD-10 Mapping
- Mucocutaneous lymph node syndrome [Kawasaki] [ICD-10 Sub-category]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]

Keyword's position in hierarchy(ies) :

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