Sezary Syndrome

Preferred Label : Sezary Syndrome;

NCIt synonyms : Sezary's Disease; Sézary Syndrome;

NCIt related terms : CTCL / Sezary syndrome; Cutaneous T-cell lymphoma/Sezary syndrome; Sezary disease; Sezary disease, unspecified site;

NCIt definition : A generalized peripheral (mature) T-cell neoplasm characterized by the presence of erythroderma, lymphadenopathy, and neoplastic, cerebriform T-lymphocytes in the blood. Sezary syndrome is an aggressive disease. (WHO, 2001);

Alternative definition : NCI-GLOSS: A form of cutaneous T-cell lymphoma, a cancerous disease that affects the skin.;

Neoplastic status : Malignant;

ICD-O code : 9701/3;

Codes from synonyms : 10011677; CDR0000045878; C84.10;

Details

Origin ID

C3366;

UMLS CUI

C0036920;

Automatic exact mappings (from CISMeF team)
- Sezary syndrome [ICD-11 More detail]
- Sezary's disease [DO Concept]
- Sezary's disease [ICD-9 code]
- Sezary's disease [ICD-9 code]
Currated CISMeF NLP mapping
- Sezary syndrome [PASCAL descriptor]
- Sezary syndrome [Disease (Nov.)]
- Sezary syndrome [ICD-O code]
- Sezary syndrome [MedDRA LLT]
- Sezary's disease [MedDRA LLT]
- Sezary's syndrome [MedDRA LLT]
- Sézary disease [ICD-10 Sub-category]
- Sézary syndrome [ICD-11 Category]
- Sézary syndrome [ORDO Disease]
- Sézary's disease (morphologic abnormality) [SNOMED CT concept]
- Sézarys disease [ICD-10 Sub-category (who)]
- sezary syndrome [MeSH Descriptor]
- sezary syndrome [MeSH concept]
- sezary's disease [SNOMED Notion]
DO Cross reference
- Sezary's disease [DO Concept]
Disease excludes abnormal cell
- Leukemic Plasma Cell [NCIt concept]
- Neoplastic B-Lymphocyte [NCIt concept]
- Reed-Sternberg Cell [NCIt concept]
Disease excludes normal cell origin
- Myeloid Cell [NCIt concept]
- Plasma Cell [NCIt concept]
- Precursor Natural Killer Cell [NCIt concept]
- Precursor T-Lymphoblast [NCIt concept]
Disease may have findings
- Alopecia [NCIt concept]
- Hyperkeratosis [NCIt concept]
- Pruritus [NCIt concept]
False automatic mappings
- Sézary's disease (disorder) [SNOMED CT concept]
Has associated anatomic sites
- Hematopoietic System [NCIt concept]
- Hematopoietic and Lymphatic System [NCIt concept]
- Skin [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Sezary syndrome [ICD-O code]
- Sezary syndrome [PASCAL descriptor]
- Sezary syndrome [Disease (Nov.)]
- Sezary syndrome [MedDRA LLT]
- Sezary's disease [ICD-9 code]
- Sezary's disease [MedDRA LLT]
- Sezary's disease [DO Concept]
- Sezary's syndrome [MedDRA LLT]
- Sézary disease [ICD-10 Sub-category]
- Sézary syndrome [ORDO Disease]
- Sézary's disease (disorder) [SNOMED CT concept]
- Sézary's disease (morphologic abnormality) [SNOMED CT concept]
- Sézarys disease [ICD-10 Sub-category (who)]
- sezary syndrome [MeSH concept]
- sezary syndrome [MeSH Descriptor]
- sezary's disease [SNOMED Notion]
concept_is_in_subset
- CPTAC Codelists Terminology [NCIt concept]
- CPTAC Neoplasms Codelist [NCIt concept]
- CPTAC Terminology [NCIt concept]
- CTRP Disease Terminology [NCIt concept]
- CTRP Terminology [NCIt concept]
- Cellosaurus Disease Terminology [NCIt concept]
- Cellosaurus Terminology [NCIt concept]
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology Terminology [NCIt concept]
- Mapped ICDO3.1 Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
- NCI CTEP SDC Non-Hodgkin Lymphoma Sub-Category Terminology [NCIt concept]
- NCI CTEP Simplified Disease Classification Terminology [NCIt concept]
- NCIt Neoplasm Core Terminology [NCIt concept]
- mCode Cancer Disorder Value Set [NCIt concept]
- mCode Elixhauser Lymphoma Value Set [NCIt concept]
- mCode Primary Cancer Disorder Value Set [NCIt concept]
- mCode Primary Malignant Neoplasm Disorder Value Set [NCIt concept]
- mCode Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Solid Growth Pattern [NCIt concept]
disease_has_abnormal_cell
- Abnormal Lymphocyte [NCIt concept]
- Cerebriform Lymphocyte [NCIt concept]
- Leukemic Cell [NCIt concept]
- Leukemic Lymphocyte [NCIt concept]
- Malignant Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Hematopoietic and Lymphoid Cell [NCIt concept]
- Neoplastic Lymphocyte [NCIt concept]
- Neoplastic T-Lymphocyte and Neoplastic Natural Killer Cell [NCIt concept]
- Sezary Cell [NCIt concept]
disease_has_associated_gene
- BCL10 Gene [NCIt concept]
- BCL10 wt Allele [NCIt concept]
disease_has_finding
- Cutaneous Involvement [NCIt concept]
- Lymphadenopathy [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Peripheral Blood Involvement [NCIt concept]
disease_has_normal_cell_origin
- Hematopoietic and Lymphoid Cell [NCIt concept]
- Lymphocyte [NCIt concept]
- Peripheral (Post-Thymic) T-Lymphocyte and Natural Killer Cell [NCIt concept]
- Peripheral Epidermotropic T-Lymphocyte [NCIt concept]
- T-Lymphocyte and Natural Killer Cell [NCIt concept]
disease_has_normal_tissue_origin
- Hematopoietic and Lymphoid Tissue [NCIt concept]
- Lymphoid Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Bone Marrow [NCIt concept]
- Hematopoietic and Lymphatic System [NCIt concept]
- Lymphatic System [NCIt concept]
disease_may_have_associated_disease
- Erythroderma [NCIt concept]
disease_may_have_molecular_abnormality
- Clonal T-Cell Receptor Beta Chain Gene Rearrangement [NCIt concept]
- Clonal T-Cell Receptor Gamma Chain Gene Rearrangement [NCIt concept]

Keyword's position in hierarchy(ies) :

You can consult :

recommendations
documents concerning education
documents for patients