" /> Polyarteritis Nodosa - CISMeF





Preferred Label : Polyarteritis Nodosa;

NCIt synonyms : PAN; Classical Polyarteritis Nodosa; Panarteritis Nodosa; Periarteritis Nodosa;

NCIt related terms : Classic Polyarteritis Nodosa;

NCIt definition : A necrotizing vasculitis that affects medium-sized arteries, it is usually idiopathic, and may be triggered by viral infections (Hepatitis B, also others). A multisystem disease, it most commonly affects skin (nodules, livedo reticularis) and peripheral nerves; higher morbidity is associated with gastrointestinal, central nervous system, cardiac, and/or other organ involvement. Anti-neutrophil cytoplasmic antibodies (ANCA) are typically negative.;

Codes from synonyms : M30.0;

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31/07/2025


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