ICD-11 code : 4A44.4;
Preferred Label : Polyarteritis nodosa;
ICD-11 definition : Polyarteritis nodosa is an immunologically mediated systemic necrotising vasculitis
affecting medium-sized vessels. In a few cases, the disease appears after viral infection
but in the majority of cases there is no known triggering event. The clinical manifestations
involve numerous organs and lead to a general alteration in the health status including
rapid weight loss, paralysis of the peripheral nerves, renal disease, and digestive
problems such as haemorrhages, perforation, appendicitis and pancreatitis. Arthralgia
is almost always present and myalgia occurs in half of patients. Cardiac and cerebral
anomalies (cephalalgia) are also reported, as well as ocular and genital (orchitis)
manifestations.;
ICD-11 synonym : Kussmaul disease; periarteritis nodosa; panarteritis nodosa; PAN - [polyarteritis nodosa];
ICD-11 acronym : PAN;
ICD-11 inclusion : polyangiitis; periarteritis nodosa with necrosis; panangiitis; arteritis nodosa; polyneuropathy in polyarteritis nodosa;
Origin ID : 1419332129;
Automatic exact mappings (from CISMeF team)
- Currated CISMeF NLP mapping
- ICD-10 Mapping
Polyarteritis nodosa is an immunologically mediated systemic necrotising vasculitis
affecting medium-sized vessels. In a few cases, the disease appears after viral infection
but in the majority of cases there is no known triggering event. The clinical manifestations
involve numerous organs and lead to a general alteration in the health status including
rapid weight loss, paralysis of the peripheral nerves, renal disease, and digestive
problems such as haemorrhages, perforation, appendicitis and pancreatitis. Arthralgia
is almost always present and myalgia occurs in half of patients. Cardiac and cerebral
anomalies (cephalalgia) are also reported, as well as ocular and genital (orchitis)
manifestations.
