" /> Pineoblastoma miRNA Processing Altered 2 - CISMeF





Preferred Label : Pineoblastoma miRNA Processing Altered 2;

NCIt synonyms : Pineoblastioma-miRNA2; PB-miRNA2; Pineoblastoma miRNA Processing Altered Group 2;

NCIt definition : Pineoblastoma characterized by alterations in genes involved in miRNA biogenesis (DICER1, DROSHA, and DGCR8). It may manifest as a sporadic tumor or part of DICER1 syndrome. It affects older children and follows a more favorable course.;

Neoplastic status : Malignant;

NCI Metathesaurus CUI : CL1921424;

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30/07/2025


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