Systemic Hydroa Vacciniforme Lymphoproliferative Disorder

Preferred Label : Systemic Hydroa Vacciniforme Lymphoproliferative Disorder;

NCIt synonyms : Systemic HV LPD; Systemic HV-LPD;

NCIt definition : Hydroa vacciniforme lymphoproliferative disorder characterized by severe clinical course and associated with fever, lymph node involvement, and involvement of internal organs by EBV-positive T-cells and NK-cells. It usually affects Asian and Latin American individuals.;

Neoplastic status : Undetermined;

NCI Metathesaurus CUI : CL1906577;

Details

Origin ID

C199677;

UMLS CUI

C5855738;

Disease excludes abnormal cell
- Neoplastic B-Lymphocyte [NCIt concept]
Disease excludes normal cell origin
- Myeloid Cell [NCIt concept]
- Precursor Natural Killer Cell [NCIt concept]
- Precursor T-Lymphoblast [NCIt concept]
Has associated anatomic sites
- Hematopoietic and Lymphatic System [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
disease_excludes_finding
- Indolent Clinical Course [NCIt concept]
- Stable Disease [NCIt concept]
disease_has_abnormal_cell
- Abnormal Lymphocyte [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Hematopoietic and Lymphoid Cell [NCIt concept]
- Neoplastic Lymphocyte [NCIt concept]
- Neoplastic T-Lymphocyte [NCIt concept]
- Neoplastic T-Lymphocyte and Neoplastic Natural Killer Cell [NCIt concept]
disease_has_associated_disease
- EBV Infection [NCIt concept]
disease_has_finding
- CD8-Positive Neoplastic Cells Present [NCIt concept]
- Childhood Lesion [NCIt concept]
- EBV-Positive Neoplastic Cells Present [NCIt concept]
- Epstein-Barr Virus Positive [NCIt concept]
- Papulovesicular Lesion [NCIt concept]
- Systemic Disease [NCIt concept]
disease_has_normal_cell_origin
- Cytotoxic T-Lymphocyte [NCIt concept]
- Hematopoietic and Lymphoid Cell [NCIt concept]
- Lymphocyte [NCIt concept]
- Peripheral (Post-Thymic) T-Lymphocyte and Natural Killer Cell [NCIt concept]
- T-Lymphocyte and Natural Killer Cell [NCIt concept]
disease_has_normal_tissue_origin
- Hematopoietic and Lymphoid Tissue [NCIt concept]
- Lymphoid Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Hematopoietic and Lymphatic System [NCIt concept]
- Lymphatic System [NCIt concept]

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