Fetal Lung Interstitial Tumor

Preferred Label : Fetal Lung Interstitial Tumor;

NCIt synonyms : FLIT;

NCIt definition : A congenital benign tumor of lung interstitial mesenchymal cells that presents with respiratory symptoms in neonates. Images reveal a well-circumscribed solid or partially cystic lung mass. Microscopical examination reveals widened alveolar septa that contain bland, uniform mesenchymal cells. Some cases show ALK rearrangement and A2M-ALK gene fusion.;

Neoplastic status : Benign;

NCI Metathesaurus CUI : CL1798823;

Details

Origin ID

C190105;

UMLS CUI

C5679952;

Currated CISMeF NLP mapping
- Fetal lung interstitial tumor [ORDO Disease]
- Fetal lung interstitial tumour [ICD-11 More detail]
Disease excludes abnormal cell
- Adenocarcinoma Cell [NCIt concept]
- Malignant Cell [NCIt concept]
- Malignant Connective and Soft Tissue Cell [NCIt concept]
- Malignant Squamous Cell [NCIt concept]
- Malignant Transitional Cell [NCIt concept]
- Neoplastic Lymphocyte [NCIt concept]
Disease may have findings
- Cystic Lesion [NCIt concept]
- Solid Lesion [NCIt concept]
Excludes anatomical site(s)
- Neck [NCIt concept]
Has associated anatomic sites
- Lung [NCIt concept]
- Respiratory System [NCIt concept]
- Thoracic Cavity [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
disease_excludes_finding
- Malignant Cellular Infiltrate [NCIt concept]
disease_has_abnormal_cell
- Neoplastic Cell [NCIt concept]
- Neoplastic Connective and Soft Tissue Cell [NCIt concept]
disease_has_finding
- Benign Cellular Infiltrate [NCIt concept]
- Childhood Lesion [NCIt concept]
- Congenital Lesion [NCIt concept]
disease_has_normal_tissue_origin
- Lung Interstitial Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Lung [NCIt concept]
- Respiratory System [NCIt concept]
- Thoracic Cavity [NCIt concept]
disease_mapped_to_gene
- A2M/ALK Fusion Gene [NCIt concept]
disease_may_have_molecular_abnormality
- ALK Gene Rearrangement [NCIt concept]

Keyword's position in hierarchy(ies) :

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