" /> EBV-Positive Inflammatory Follicular Dendritic Cell/Fibroblastic Reticular Cell Tumor - CISMeF





Preferred Label : EBV-Positive Inflammatory Follicular Dendritic Cell/Fibroblastic Reticular Cell Tumor;

NCIt synonyms : Epstein-Barr Virus-Positive Inflammatory Follicular Dendritic Cell Sarcoma; Inflammatory Pseudotumor-Like Follicular/Fibroblastic Dendritic Cell Sarcoma; Epstein-Barr Virus Positive Inflammatory Follicular Dendritic Cell Sarcoma; IPT-Like FDCS; EBV-Positive Inflammatory Follicular Dendritic Cell Sarcoma; Epstein-Barr Virus Positive Inflammatory Follicular Dendritic Cell/Fibroblastic Reticular Cell Tumor; Epstein-Barr Virus-Positive Inflammatory Follicular Dendritic Cell/Fibroblastic Reticular Cell Tumor;

NCIt definition : A rare, Epstein-Barr virus-associated variant of follicular dendritic cell sarcoma. It usually arises from the liver or spleen and has a favorable prognosis. The name of this entity has been changed from sarcoma to tumor because of its indolent nature.;

Neoplastic status : Malignant;

NCI Metathesaurus CUI : CL1406871;

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30/07/2025


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