EBV-Positive Inflammatory Follicular Dendritic Cell/Fibroblastic Reticular Cell Tumor

Preferred Label : EBV-Positive Inflammatory Follicular Dendritic Cell/Fibroblastic Reticular Cell Tumor;

NCIt synonyms : Epstein-Barr Virus-Positive Inflammatory Follicular Dendritic Cell Sarcoma; Inflammatory Pseudotumor-Like Follicular/Fibroblastic Dendritic Cell Sarcoma; Epstein-Barr Virus Positive Inflammatory Follicular Dendritic Cell Sarcoma; IPT-Like FDCS; EBV-Positive Inflammatory Follicular Dendritic Cell Sarcoma; Epstein-Barr Virus Positive Inflammatory Follicular Dendritic Cell/Fibroblastic Reticular Cell Tumor; Epstein-Barr Virus-Positive Inflammatory Follicular Dendritic Cell/Fibroblastic Reticular Cell Tumor;

NCIt definition : A rare, Epstein-Barr virus-associated variant of follicular dendritic cell sarcoma. It usually arises from the liver or spleen and has a favorable prognosis. The name of this entity has been changed from sarcoma to tumor because of its indolent nature.;

Neoplastic status : Malignant;

NCI Metathesaurus CUI : CL1406871;

Details

Origin ID

C172847;

UMLS CUI

C5419896;

Disease excludes normal cell origin
- Epithelial Cell [NCIt concept]
Disease may have findings
- Asymptomatic Mass [NCIt concept]
- CD21-Positive Neoplastic Cells Present [NCIt concept]
- CD35-Positive Neoplastic Cells Present [NCIt concept]
- CD68-Positive Neoplastic Cells Present [NCIt concept]
- Indolent Clinical Course [NCIt concept]
- Lymphadenopathy [NCIt concept]
- S-100-Positive Neoplastic Cells Present [NCIt concept]
Excludes anatomical site(s)
- Bone [NCIt concept]
Has associated anatomic sites
- Connective and Soft Tissue [NCIt concept]
- Hematopoietic and Lymphatic System [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Birbeck Granules Present [NCIt concept]
- CD1a-Positive Neoplastic Cells Present [NCIt concept]
- CD30-Positive Neoplastic Cells Present [NCIt concept]
- HMB-45-Positive Neoplastic Cells Present [NCIt concept]
- Indolent Clinical Course [NCIt concept]
- Intermediate Filaments Present [NCIt concept]
- Intracytoplasmic Eosinophilic Inclusion [NCIt concept]
disease_excludes_molecular_abnormality
- Clonal Immunoglobulin Gene Rearrangement [NCIt concept]
- Clonal T-Cell Receptor Gene Rearrangement [NCIt concept]
disease_excludes_normal_tissue_origin
- Epithelial Tissue [NCIt concept]
disease_has_abnormal_cell
- Malignant Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Follicular Dendritic Cell [NCIt concept]
- Neoplastic Hematopoietic and Lymphoid Cell [NCIt concept]
- Neoplastic Histiocytic and Dendritic Cell [NCIt concept]
- Neoplastic Spindle Cell [NCIt concept]
disease_has_associated_disease
- EBV Infection [NCIt concept]
- Infectious Disorder [NCIt concept]
- Viral Infection [NCIt concept]
disease_has_finding
- EBV-Positive Neoplastic Cells Present [NCIt concept]
- Favorable Clinical Outcome [NCIt concept]
- Histiocytosis [NCIt concept]
- Lymphoplasmacytic Infiltrate [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Rare Lesion [NCIt concept]
- Storiform Growth Pattern [NCIt concept]
- Whorling Growth Pattern [NCIt concept]
disease_has_normal_cell_origin
- Follicular Dendritic Cell [NCIt concept]
- Hematopoietic and Lymphoid Cell [NCIt concept]
- Histiocyte [NCIt concept]
- Histiocytic and Dendritic Cell [NCIt concept]
disease_has_normal_tissue_origin
- Connective and Soft Tissue [NCIt concept]
- Germinal Center [NCIt concept]
- Hematopoietic and Lymphoid Tissue [NCIt concept]
- Soft Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Hematopoietic and Lymphatic System [NCIt concept]
disease_may_have_associated_disease
- Castleman Disease [NCIt concept]
disease_may_have_molecular_abnormality
- BRAF Gene Mutation [NCIt concept]

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