" /> Pituitary Gland Blastoma - CISMeF





Preferred Label : Pituitary Gland Blastoma;

NCIt synonyms : Pituitary Gland Embryoma; Pituitary Embryoma; Pituitary Blastoma;

NCIt definition : A rare developmental early childhood neoplasm, arising within the fetal anterior pituitary. It is associated with DICER1 mutations. Patients present with features of Cushing disease, with elevated blood ACTH levels and hypercortisolism. Ophthalmoplegia is a frequent symptom. The overall prognosis is poor. (WHO);

Neoplastic status : Malignant;

NCI Metathesaurus CUI : CL555935;

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29/07/2025


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