Preferred Label : Stage IVA1;
NCIt related terms : IVA2;
NCIt definition : A mycosis fungoides/Sezary syndrome stage defined as follows: T1-4, N0-2, M0, B2.
T1: Limited patches, papules, and/or plaques covering less than 10% of the skin surface.
T2: Patches, papules, or plaques covering 10% or more of the skin surface. T3: One
or more tumors (equal or greater than 1 cm in diameter). T4: Confluence of erythema
covering 80% or more of body surface area. N0: No clinically abnormal peripheral lymph
nodes; biopsy not required. N1: Clinically abnormal peripheral lymph nodes; histopathology
Dutch grade 1 or National Cancer Institute (NCI) LN0-2. N2: Clinically abnormal peripheral
lymph nodes; histopathology Dutch grade 2 or NCI LN3. M0: No visceral organ involvement.
B2: High blood tumor burden: 1,000 per microliter or more Sezary cells with positive
clone. (AJCC 8th ed.);
Origin ID : C141344;
UMLS CUI : C3869907;
Semantic type(s)
- is_stage_of_disease
