Synovitis, Acne, Pustulosis, Hyperostosis, and Osteitis Syndrome

Preferred Label : Synovitis, Acne, Pustulosis, Hyperostosis, and Osteitis Syndrome;

NCIt synonyms : PPHS;

NCIt related terms : SAPHO Syndrome; Pustulo-Psoriatic Hyperostotic Spondyloarthritis;

Alternative definition : NICHD: A syndrome characterized by synovitis, acne, pustulosis, hyperostosis, and non-infectious osteomyelitis. Includes a spectrum of aseptic neutrophilic dermatoses associated with aseptic osteoarticular lesions.;

NCI Metathesaurus CUI : CL480775;

Details

Origin ID

C119049;

UMLS CUI

C0263859;

Currated CISMeF NLP mapping
- SAPHO syndrome [MedDRA Preferred Term]
- SAPHO syndrome [ICD-11 Category]
- SAPHO syndrome [DO Concept]
- SAPHO syndrome [ORDO Disease]
- SAPHO syndrome [PASCAL descriptor]
- Synovitis acne pustulosis hyperostosis osteomyelitis syndrome (disorder) [SNOMED CT concept]
- acquired hyperostosis syndrome [MeSH Descriptor]
- acquired hyperostosis syndrome [MeSH concept]
- sapho syndrome [SNOMED Notion]
DO Cross reference
- SAPHO syndrome [DO Concept]
False automatic mappings
- Other immediate postpartum haemorrhage [ICD-11 Subcategory]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
UMLS correspondences (same concept)
- SAPHO syndrome [ORDO Disease]
- SAPHO syndrome [PASCAL descriptor]
- SAPHO syndrome [DO Concept]
- SAPHO syndrome [MedDRA Preferred Term]
- SAPHO syndrome [ICD-11 Category]
- Synovitis acne pustulosis hyperostosis osteomyelitis syndrome (disorder) [SNOMED CT concept]
- acquired hyperostosis syndrome [MeSH Descriptor]
- acquired hyperostosis syndrome [MeSH concept]
- sapho syndrome [SNOMED Notion]
concept_is_in_subset
- NICHD Terminology [NCIt concept]
- Pediatric Rheumatology Terminology [NCIt concept]

Keyword's position in hierarchy(ies) :

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