SAPHO syndrome

ICD-11 code : 4A61;

Preferred Label : SAPHO syndrome;

ICD-11 definition : SAPHO syndrome is characterized by a constellation of symptoms and signs including synovitis, acne conglobata or fulminans, palmoplantar pustulosis, hyperostosis and osteitis. Its aetiology is poorly understood.;

ICD-11 synonym : Pustulo-psoriatic hyperostotic spondylarthritis; SAPHO - [synovitis, acne, pustulosis, hyperostosis, osteitis] syndrome;

ICD-11 inclusion : Juvenile chronic recurrent multifocal osteomyelitis;

Details

Origin ID

1901494067;

UMLS CUI

C0263859;

Currated CISMeF NLP mapping
- Acquired Hyperostosis Syndrome [NCIt concept]
- SAPHO syndrome [DO Concept]
- SAPHO syndrome [MedDRA Preferred Term]
- SAPHO syndrome [ORDO Disease]
- SAPHO syndrome [PASCAL descriptor]
- Synovitis acne pustulosis hyperostosis osteomyelitis syndrome (disorder) [SNOMED CT concept]
- Synovitis, Acne, Pustulosis, Hyperostosis, and Osteitis Syndrome [NCIt concept]
- acquired hyperostosis syndrome [MeSH Descriptor]
- acquired hyperostosis syndrome [MeSH concept]
- sapho syndrome [SNOMED Notion]
ICD-10 Mapping
- Chronic multifocal osteomyelitis [ICD-10 Sub-category]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
UMLS correspondences (same concept)
- Acquired Hyperostosis Syndrome [NCIt concept]
- SAPHO syndrome [DO Concept]
- SAPHO syndrome [MedDRA Preferred Term]
- SAPHO syndrome [ORDO Disease]
- SAPHO syndrome [PASCAL descriptor]
- Synovitis acne pustulosis hyperostosis osteomyelitis syndrome (disorder) [SNOMED CT concept]
- Synovitis, Acne, Pustulosis, Hyperostosis, and Osteitis Syndrome [NCIt concept]
- acquired hyperostosis syndrome [MeSH Descriptor]
- acquired hyperostosis syndrome [MeSH concept]
- sapho syndrome [SNOMED Notion]

Keyword's position in hierarchy(ies) :

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