" /> SAPHO syndrome - CISMeF





ICD-11 code : 4A61;

Preferred Label : SAPHO syndrome;

ICD-11 definition : SAPHO syndrome is characterized by a constellation of symptoms and signs including synovitis, acne conglobata or fulminans, palmoplantar pustulosis, hyperostosis and osteitis. Its aetiology is poorly understood.;

ICD-11 synonym : Pustulo-psoriatic hyperostotic spondylarthritis; SAPHO - [synovitis, acne, pustulosis, hyperostosis, osteitis] syndrome;

ICD-11 inclusion : Juvenile chronic recurrent multifocal osteomyelitis;

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SAPHO syndrome is characterized by a constellation of symptoms and signs including synovitis, acne conglobata or fulminans, palmoplantar pustulosis, hyperostosis and osteitis. Its aetiology is poorly understood.

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31/07/2025


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