" /> 2-methyl-3-hydroxybutyryl-coenzyme A dehydrogenase - CISMeF





Preferred Label : 2-methyl-3-hydroxybutyryl-coenzyme A dehydrogenase;

MeSH note : reaction:(2S,3S)-3-hydroxy-2-methylbutanoyl-CoA NAD 2-methylacetoacetyl-CoA NADH; deficiency is associated with progressive infantile neurodegeneration;

MeSH synonym : (2S,3S)-3-hydroxy-2-methylbutanoyl-CoA NAD - oxidoreductase; 2-MHB-CoA dehydrogenase; 2-methyl-3-hydroxybutyryl-CoA dehydrogenase;

Registry Number MeSH : EC 1.1.1.178;

Is substance : O;

UNII : EC 1.1.1.178;

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27/07/2025


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