mitochondrial trifunctional protein

Preferred Label : mitochondrial trifunctional protein;

MeSH definition : A mitochondrial protein consisting of four alpha-subunits and four beta-subunits. It contains enoyl-CoA hydratase, long-chain-3-hydroxyacyl-CoA dehydrogenase, and acetyl-CoA C-acyltransferase activities and plays an important role in the metabolism of long chain FATTY ACIDS.;

MeSH synonym : trifunctional protein, mitochondrial; mitochondrial long chain enoyl CoA hydratase 3 hydroxyacyl CoA dehydrogenase 3 ketoacyl CoA thiolase trifunctional protein; FA beta-OMC; mitochondrial fatty acid beta-Oxidation trifunctional protein; mitochondrial fatty acid beta oxidation trifunctional protein;

MeSH Related Number : EC 1.1.1.211; EC 4.2.1.17;

Registry Number MeSH : EC 2.3.1.16;

Is substance : O;

UNII : EC 2.3.1.16;

Details

Origin ID

D063991;

UMLS CUI

C3658275;

Allowable qualifiers
- administration and dosage [MeSH Qualifier]
- adverse effects [MeSH Qualifier]
- analysis [MeSH Qualifier]
- antagonists and inhibitors [MeSH Qualifier]
- biosynthesis [MeSH Qualifier]
- blood [MeSH Qualifier]
- cerebrospinal fluid [MeSH Qualifier]
- chemical synthesis [MeSH Qualifier]
- chemistry [MeSH Qualifier]
- classification [MeSH Qualifier]
- contraindications [MeSH Qualifier]
- deficiency [MeSH Qualifier]
- drug effects [MeSH Qualifier]
- economics [MeSH Qualifier]
- genetics [MeSH Qualifier]
- history [MeSH Qualifier]
- immunology [MeSH Qualifier]
- isolation and purification [MeSH Qualifier]
- metabolism [MeSH Qualifier]
- pharmacokinetics [MeSH Qualifier]
- pharmacology [MeSH Qualifier]
- physiology [MeSH Qualifier]
- poisoning [MeSH Qualifier]
- radiation effects [MeSH Qualifier]
- standards [MeSH Qualifier]
- supply and distribution [MeSH Qualifier]
- therapeutic use [MeSH Qualifier]
- toxicity [MeSH Qualifier]
- ultrastructure [MeSH Qualifier]
- urine [MeSH Qualifier]
Automatic exact mappings (from CISMeF team)
- hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha [HGNC gene]
- hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta [HGNC gene]
Record concept(s)
- mitochondrial trifunctional protein [MeSH concept]
Related MeSH Supplementary Concept(s)
- trifunctional protein deficiency with myopathy and neuropathy [MeSH Supplementary Concept]
Semantic type(s)
- Amino Acid, Peptide, or Protein [UMLS semantic type]
- Enzyme [UMLS semantic type]

Keyword's position in hierarchy(ies) :

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