isolated noncompaction of the ventricular myocardium

Preferred Label : isolated noncompaction of the ventricular myocardium;

MeSH definition : Rare congenital cardiomyopathies characterized by the lack of left ventricular myocardium compaction. The noncompaction results in numerous prominent trabeculations and a loose myocardial meshwork (spongy myocardium) in the LEFT VENTRICLE. Heterogeneous clinical features include diminished systolic function sometimes associated with left ventricular dilation, that presents either neonatally or progressively. Often, the RIGHT VENTRICLE is also affected. CONGESTIVE HEART FAILURE; PULMONARY EMBOLISM; and ventricular ARRHYTHMIA are commonly seen.;

MeSH synonym : isolated non-compaction of the ventricular myocardium;

MeSH hyponym : noncompaction of the left ventricular myocardium, autosomal dominant; isolated noncompaction of the left ventricular myocardium, X-Linked;

Details

Origin ID

D056830;

UMLS CUI

C2717907;

Allowable qualifiers
- blood [MeSH Qualifier]
- cerebrospinal fluid [MeSH Qualifier]
- chemically induced [MeSH Qualifier]
- classification [MeSH Qualifier]
- complications [MeSH Qualifier]
- diagnosis [MeSH Qualifier]
- diagnostic imaging [MeSH Qualifier]
- diet therapy [MeSH Qualifier]
- drug therapy [MeSH Qualifier]
- economics [MeSH Qualifier]
- embryology [MeSH Qualifier]
- enzymology [MeSH Qualifier]
- epidemiology [MeSH Qualifier]
- ethnology [MeSH Qualifier]
- etiology [MeSH Qualifier]
- genetics [MeSH Qualifier]
- history [MeSH Qualifier]
- immunology [MeSH Qualifier]
- metabolism [MeSH Qualifier]
- microbiology [MeSH Qualifier]
- mortality [MeSH Qualifier]
- nursing [MeSH Qualifier]
- parasitology [MeSH Qualifier]
- pathology [MeSH Qualifier]
- physiopathology [MeSH Qualifier]
- prevention and control [MeSH Qualifier]
- psychology [MeSH Qualifier]
- radiotherapy [MeSH Qualifier]
- rehabilitation [MeSH Qualifier]
- surgery [MeSH Qualifier]
- therapy [MeSH Qualifier]
- urine [MeSH Qualifier]
- veterinary [MeSH Qualifier]
- virology [MeSH Qualifier]
Record concept(s)
- isolated noncompaction of the left ventricular myocardium, X-Linked [MeSH concept]
- isolated noncompaction of the ventricular myocardium [MeSH concept]
- noncompaction of the left ventricular myocardium, autosomal dominant [MeSH concept]
Related MeSH Supplementary Concept(s)
- cardiomyopathy, dilated, with left ventricular noncompaction [MeSH Supplementary Concept]
- noncompaction of left ventricular myocardium, familial isolated, autosomal dominant 1 [MeSH Supplementary Concept]
- noncompaction of left ventricular myocardium, familial isolated, autosomal dominant 2 [MeSH Supplementary Concept]
See also
- barth syndrome [MeSH Descriptor]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]

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