Preferred Label : Acyl-CoA dehydrogenase;

MeSH definition : A flavoprotein oxidoreductase that has specificity for medium-chain fatty acids. It forms a complex with ELECTRON TRANSFERRING FLAVOPROTEINS and conveys reducing equivalents to UBIQUINONE.;

MeSH synonym : medium chain acyl coa dehydrogenase; acyl-coenzyme a dehydrogenase; mcaca-dehydrogenase; dehydrogenase, palmitoyl-coa; dehydrogenase, medium-chain acyl-coa; palmitoyl coa dehydrogenase; dehydrogenase, acyl-coa; fatty-acyl coa dehydrogenase; coa dehydrogenase, fatty-acyl; dehydrogenase, fatty-acyl coa; fatty acyl coa dehydrogenase; palmitoyl-coa dehydrogenase; medium chain acyl-coa dehydrogenase; medium-chain acyl-coenzyme a dehydrogenase; medium chain acyl coenzyme a dehydrogenase; octanoyl-coa dehydrogenase; dehydrogenase, octanoyl-coa; octanoyl coa dehydrogenase; medium-chain acyl-coa dehydrogenase; acyl-coa dehydrogenase, medium-chain; acyl coenzyme a dehydrogenase; dehydrogenase, acyl-coenzyme a; mcaca dehydrogenase; acyl CoA dehydrogenase;

CISMeF synonym : EC 1.3.99.3;

MeSH Related Number : 9027-65-0 (CRN); EC 1.3.8.8; EC 1.3.8.9;

Registry Number MeSH : EC 1.3.99.3; EC 1.3.8.7;

MeSH annotation : ACYL-COA DEHYDROGENASES and ACYL-COA DEHYDROGENASE, LONG-CHAIN are also available;

Wikipedia link : https://en.wikipedia.org/wiki/Acyl-coa dehydrogenase;

Is substance : O;

UNII : EC 1.3.8.7;

Details


Main resources

You can consult :

A flavoprotein oxidoreductase that has specificity for medium-chain fatty acids. It forms a complex with ELECTRON TRANSFERRING FLAVOPROTEINS and conveys reducing equivalents to UBIQUINONE.

https://publications.msss.gouv.qc.ca/msss/document-001995/
2025
Canada
algorithms
Acyl-CoA dehydrogenase
fatty acid, nos
acyl-coa dehydrogenase deficiency, nos
diagnosis
fatty acids
COA protocol
chain
COA protocol

---
https://www.orpha.net/data/patho/Emg/Int/fr/DeficitMCAD_FR_fr_EMG_ORPHA42.pdf
2021
France
guideline
snacks
Fatty acids
medium chain fatty acid, nos
Acyl-CoA dehydrogenase deficiency
acyl-coa dehydrogenase deficiency, nos
fatty acids
emergencies
Practice
cranioosteoarthropathy
best practices
Acyl-CoA dehydrogenase

---
http://publications.msss.gouv.qc.ca/msss/document-002130/
2018
Canada
algorithms
cranioosteoarthropathy
patient care management
diagnosis
Acyl-CoA dehydrogenase deficiency
Acyl-CoA dehydrogenase
acyl coenzyme A
chain
acyl-coa dehydrogenase deficiency, nos
osteoarthropathy, primary hypertrophic

---
http://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=FR&Expert=42
2014
false
France
French
resource guides
Acyl-CoA dehydrogenase
medium chain acyl CoA dehydrogenase deficiency
scientific and technical information

---
https://www.orpha.net/data/patho/Pub/fr/DeficitMCAD-FRfrPub3570.pdf
2014
false
false
false
France
French
patient education handout
medium chain acyl CoA dehydrogenase deficiency
Acyl-CoA dehydrogenase
lipid metabolism, inborn errors
signs and symptoms
lipid metabolism, inborn errors
lipid metabolism, inborn errors
prenatal diagnosis
lipid metabolism, inborn errors
Mainstreaming, Education

---
https://www.sfpediatrie.com/sites/www.sfpediatrie.com/files/medias/documents/deficit_mcad_0.pdf
10.1016/j.arcped.2011.10.025
2011
false
true
false
France
guideline
medium chain acyl CoA dehydrogenase deficiency
Acyl-CoA dehydrogenase
lipid metabolism, inborn errors
lipid metabolism, inborn errors
lipid metabolism, inborn errors
lipid metabolism, inborn errors
lipid metabolism, inborn errors
lipid metabolism, inborn errors
lipid metabolism, inborn errors
lipid metabolism, inborn errors
lipid metabolism, inborn errors

---
http://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=FR&Expert=99901
2011
France
scientific and technical information
Acyl-CoA dehydrogenase
acyl-coa dehydrogenase deficiency, nos

---
http://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=FR&Expert=99900
2011
France
scientific and technical information
Acyl-CoA dehydrogenase

---
http://www.has-sante.fr/portail/jcms/c_1069254/evaluation-de-lextension-du-depistage-neonatal-a-une-ou-plusieurs-erreurs-innees-du-metabolisme-par-spectrometrie-de-masse-en-tandem-1er-volet-deficit-en-mcad
http://www.has-sante.fr/portail/jcms/c_1069331/argumentaire-evaluation-a-priori-de-l-extension-du-depistage-neonatal-a-une-ou-plusieurs-erreurs-innees-du-metabolisme-par-la-technique-de-spectrometrie-de-masse-en-tandem-en-population-generale-1er-volet-depistage-du-deficit-en-mcad
2011
true
France
French
public health evaluation
health technology assessment
public health guidelines
economic evaluation
neonatal screening
infant, newborn
metabolism, inborn errors
mass spectrometry
europe
european union
united states
canada
australia
Acyl-CoA dehydrogenase
phenylketonurias
neonatal screening
neonatal screening
neonatal screening
neonatal screening
Cost-Benefit analysis
program evaluation

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24/05/2025


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