Preferred Label : pyruvate dehydrogenase (lipoamide);

MeSH definition : The E1 component of the multienzyme PYRUVATE DEHYDROGENASE COMPLEX. It is composed of 2 alpha subunits (pyruvate dehydrogenase E1 alpha subunit) and 2 beta subunits (pyruvate dehydrogenase E1 beta subunit).;

MeSH synonym : pyruvate dehydrogenase component e1; pyruvate dehydrogenase-e1; pyruvate dehydrogenase e1; pyruvate decarboxylase (lipoamide);

MeSH Related Number : 9014-20-4 (CRN);

Registry Number MeSH : EC 1.2.4.1;

Is substance : O;

UNII : EC 1.2.4.1;

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The E1 component of the multienzyme PYRUVATE DEHYDROGENASE COMPLEX. It is composed of 2 alpha subunits (pyruvate dehydrogenase E1 alpha subunit) and 2 beta subunits (pyruvate dehydrogenase E1 beta subunit).

http://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=FR&Expert=79243
2011
France
scientific and technical information
pyruvate dehydrogenase (lipoamide)
pyruvate dehydrogenase E1 alpha deficiency
pyruvate dehydrogenase complex deficiency
pyruvate dehydrogenase E1 alpha deficiency
pyruvate dehydrogenase complex deficiency disease

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http://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=FR&Expert=255138
2011
France
scientific and technical information
pyruvate dehydrogenase (lipoamide)
pyruvate dehydrogenase E1-Beta deficiency
pyruvate dehydrogenase complex deficiency disease
pyruvate dehydrogenase E1-Beta deficiency
pyruvate dehydrogenase complex deficiency

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29/04/2025


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