Preferred Label : hemangioendothelioma, epithelioid;
MeSH definition : A tumor of medium-to-large veins, composed of plump-to-spindled endothelial cells
that bulge into vascular spaces in a tombstone-like fashion. These tumors are thought
to have borderline aggression, where one-third develop local recurrences, but only
rarely metastasize. It is unclear whether the epithelioid hemangioendothelioma is
truly neoplastic or an exuberant tissue reaction, nor is it clear if this is equivalent
to Kimura's disease (see ANGIOLYMPHOID HYPERPLASIA WITH EOSINOPHILIA). (Segen, Dictionary
of Modern Medicine, 1992);
MeSH synonym : epithelioid hemangioendothelioma; epithelioid hemangioendotheliomas; hemangioendotheliomas, epithelioid;
MeSH annotation : /blood supply /chem /second /secret /ultrastruct permitted; coord IM with precoord
organ/neopl term (IM); coordinate with precoordinated organ/neoplasm term;
Origin ID : D018323;
UMLS CUI : C0206732;
Allowable qualifiers
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
ORDO relation(s)
Record concept(s)
Semantic type(s)
UMLS correspondences (same concept)
A tumor of medium-to-large veins, composed of plump-to-spindled endothelial cells
that bulge into vascular spaces in a tombstone-like fashion. These tumors are thought
to have borderline aggression, where one-third develop local recurrences, but only
rarely metastasize. It is unclear whether the epithelioid hemangioendothelioma is
truly neoplastic or an exuberant tissue reaction, nor is it clear if this is equivalent
to Kimura's disease (see ANGIOLYMPHOID HYPERPLASIA WITH EOSINOPHILIA). (Segen, Dictionary
of Modern Medicine, 1992)
http://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=FR&Expert=157791
2011
France
scientific and technical information
hemangioendothelioma, epithelioid
epithelioid hemangioendothelioma, nos
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