Preferred Label : Desmoid Tumors;
MeSH definition : A childhood counterpart of abdominal or extra-abdominal desmoid tumors, characterized
by firm subcutaneous nodules that grow rapidly in any part of the body but do not
metastasize. The adult form of abdominal fibromatosis is FIBROMATOSIS, ABDOMINAL.
(Stedman, 25th ed); Locally aggressive tumors that form in the connective tissues of body with no known
potential for metastasis. However, they are characterized by an infiltrative growth
pattern, allowing invasion into nearby tissues and organs, particularly evident in
patients with FAMILIAL ADENOMATOUS POLYPOSIS.;
MeSH synonym : fibromatoses, aggressive; aggressive fibromatoses; aggressive fibromatosis; Desmoid Tumor; Tumor, Desmoid; Tumors, Desmoid; Deep Fibromatoses; Deep Fibromatose; Fibromatose, Deep; Fibromatoses, Deep; Deep Fibromatosis; Fibromatosis, Deep; Desmoid Fibromatosis; Desmoid Fibromatoses; Fibromatoses, Desmoid; Fibromatosis, Desmoid; Desmoid-type Fibromatosis; Desmoid-type Fibromatoses; Desmoid type Fibromatosis; Fibromatoses, Desmoid-type; Fibromatosis, Desmoid-type; Fibromatosis, Aggressive;
CISMeF synonym : fibromatosis, aggressive; desmoid; desmoids;
MeSH hyponym : Fibromatoses, Musculoaponeurotic; Fibromatosis, Musculoaponeurotic; Musculoaponeurotic Fibromatoses; Extra Abdominal Desmoid Tumor;
MeSH annotation : in children; do not use /blood supply /chem /second /secret /ultrastruct; coord IM
with precoord organ/neopl term if specified (IM); coordinate with precoordinated organ/neoplasm term if specified;
Wikipedia link : https://en.wikipedia.org/wiki/Aggressive fibromatosis;
Origin ID : D018222;
UMLS CUI : C0079218;
Allowable qualifiers
Currated CISMeF NLP mapping
HPO term
Manual NTBT mappings (CISMeF)
Record concept(s)
Related MeSH Supplementary Concept(s)
Semantic type(s)
UMLS correspondences (same concept)
A childhood counterpart of abdominal or extra-abdominal desmoid tumors, characterized
by firm subcutaneous nodules that grow rapidly in any part of the body but do not
metastasize. The adult form of abdominal fibromatosis is FIBROMATOSIS, ABDOMINAL.
(Stedman, 25th ed)
Locally aggressive tumors that form in the connective tissues of body with no known
potential for metastasis. However, they are characterized by an infiltrative growth
pattern, allowing invasion into nearby tissues and organs, particularly evident in
patients with FAMILIAL ADENOMATOUS POLYPOSIS.
https://www.snfge.org/tncd/tumeurs-desmoides-localisation-abdominale-associees-polypose-adenomateuse
2022
false
false
false
France
practice guideline
Desmoid Tumors
associated with
neoplasms
abdominal fibromatosis
abdominal neoplasms
multiple polyps
---
http://oncologik.fr/referentiels/interregion/tumeurs-desmoides
2019
false
true
false
false
France
French
algorithms
Desmoid tumors
Desmoid Tumors
Desmoid Tumors
Desmoid Tumors
Desmoid Tumors
Desmoid Tumors
guideline
Desmoid Tumors
---
http://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=FR&Expert=873
http://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=FR&Expert=873
2013
true
France
French
Desmoid Tumors
scientific and technical information
---
http://www.sos-desmoide.asso.fr/
France
English
French
Desmoid Tumors
Desmoid Tumors
rare diseases
association of patients
association of health professionals
---
http://www.hopitalsaintlouis.org/index.php?option=com_content&view=article&id=111:tumeur-desmoide&catid=75:chirurgie-plastique-gennerale-ii&Itemid=57
2011
false
true
false
France
Desmoid Tumors
Desmoid Tumors
Desmoid Tumors
popular works
Desmoid Tumors
---
http://www.cancerenfants.fr/index.php?code=pJvEpKOZ0anP187T0dQ=
2006
false
France
French
Desmoid Tumors
child
Desmoid Tumors
Desmoid Tumors
patient education handout
---