immunoproliferative small intestinal disease

Preferred Label : immunoproliferative small intestinal disease;

MeSH definition : A condition that is caused by HYPERPLASIA of LYMPHOCYTES in the small intestine (INTESTINE, SMALL) and the mesenteric LYMPH NODES. These lymphocytes produce an anomalous alpha heavy chain protein. Generally, these IPSID patients have either concurrent LYMPHOMA or develop lymphoma within a few years. The disease was first described in the Mediterranean region and is characterized by malabsorption; WEIGHT LOSS; DIARRHEA; and STEATORRHEA.;

MeSH synonym : alpha chain disease; lymphoma, mediterranean; ipsid; alpha-chain disease; diseases, alpha-chain; heavy chain disease, iga type; disease, alpha-chain; mediterranean lymphoma; alpha-chain diseases;

Details

Origin ID

D007161;

UMLS CUI

C0021071;

Allowable qualifiers
- blood [MeSH Qualifier]
- cerebrospinal fluid [MeSH Qualifier]
- chemically induced [MeSH Qualifier]
- classification [MeSH Qualifier]
- complications [MeSH Qualifier]
- congenital [MeSH Qualifier]
- diagnosis [MeSH Qualifier]
- diagnostic imaging [MeSH Qualifier]
- diet therapy [MeSH Qualifier]
- drug therapy [MeSH Qualifier]
- economics [MeSH Qualifier]
- embryology [MeSH Qualifier]
- enzymology [MeSH Qualifier]
- epidemiology [MeSH Qualifier]
- ethnology [MeSH Qualifier]
- etiology [MeSH Qualifier]
- genetics [MeSH Qualifier]
- history [MeSH Qualifier]
- immunology [MeSH Qualifier]
- metabolism [MeSH Qualifier]
- microbiology [MeSH Qualifier]
- mortality [MeSH Qualifier]
- nursing [MeSH Qualifier]
- parasitology [MeSH Qualifier]
- pathology [MeSH Qualifier]
- physiopathology [MeSH Qualifier]
- prevention and control [MeSH Qualifier]
- psychology [MeSH Qualifier]
- radiotherapy [MeSH Qualifier]
- rehabilitation [MeSH Qualifier]
- surgery [MeSH Qualifier]
- therapy [MeSH Qualifier]
- urine [MeSH Qualifier]
- veterinary [MeSH Qualifier]
- virology [MeSH Qualifier]
Automatic exact mappings (from CISMeF team)
- Alpha heavy chain disease, enteric form (disorder) [SNOMED CT concept]
- Immunoproliferative small intestinal disease [ICD-11 Extension code]
- Immunoproliferative small intestinal disease [ICD-11 More detail]
- alpha chain disease [DO Concept]
Currated CISMeF NLP mapping
- Alpha Heavy Chain Disease [NCIt concept]
- Alpha heavy chain disease [ICD-11 Subcategory]
- Alpha heavy chain disease [ICD-11 Extension code]
- Alpha heavy chain disease [ICD-10 Sub-category (who)]
- Alpha heavy chain disease (disorder) [SNOMED CT concept]
- Heavy Chain Disease [NCIt concept]
- Heavy chain disease [MedDRA Preferred Term]
- Heavy chain disease (disorder) [SNOMED CT concept]
- Heavy chain disease (morphologic abnormality) [SNOMED CT concept]
- Immunoproliferative small intestinal disease [ICD-10 Sub-category]
- Immunoproliferative small intestinal disease [ICD-10 Sub-category (who)]
- Immunoproliferative small intestinal disease [ICD-O code]
- Immunoproliferative small intestinal disease [ORDO Disease]
- Immunoproliferative small intestinal disease (disorder) [SNOMED CT concept]
- Immunoproliferative small intestinal disease (morphologic abnormality) [SNOMED CT concept]
- alpha heavy chain disease [SNOMED Notion]
- heavy chain disease, nos [SNOMED Notion]
- immunoproliferative small intestinal disease [SNOMED Notion]
- immunoproliferative small intestinal disorder [Disease (Nov.)]
- α-Heavy chain disease [PASCAL descriptor]
False automatic mappings
- Heavy chain disease [ORDO Disease]
Manual NTBT mappings (CISMeF)
- Severe immune-mediated enteropathy [ORDO Disease]
ORDO relation(s)
- Immunoproliferative small intestinal disease [ORDO Disease]
Record concept(s)
- immunoproliferative small intestinal disease [MeSH concept]
See also inter- (CISMeF)
- Alpha-heavy chain disease [ORDO Disease]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Alpha Heavy Chain Disease [NCIt concept]
- Alpha heavy chain disease [ICD-10 Sub-category (who)]
- Alpha heavy chain disease (disorder) [SNOMED CT concept]
- Alpha heavy chain disease, enteric form (disorder) [SNOMED CT concept]
- Alpha-heavy chain disease [ORDO Disease]
- Immunoproliferative small intestinal disease [ORDO Disease]
- Immunoproliferative small intestinal disease [ICD-O code]
- Immunoproliferative small intestinal disease [ICD-10 Sub-category (who)]
- Immunoproliferative small intestinal disease [ICD-10 Sub-category]
- Immunoproliferative small intestinal disease (disorder) [SNOMED CT concept]
- Immunoproliferative small intestinal disease (morphologic abnormality) [SNOMED CT concept]
- alpha heavy chain disease [SNOMED Notion]
- immunoproliferative small intestinal disease [SNOMED Notion]
- immunoproliferative small intestinal disorder [Disease (Nov.)]
- α-Heavy chain disease [PASCAL descriptor]

Keyword's position in hierarchy(ies) :

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