Preferred Label : cystathionine gamma-lyase;
MeSH definition : A multifunctional pyridoxal phosphate enzyme. In the final step in the biosynthesis
of cysteine it catalyzes the cleavage of cystathionine to yield cysteine, ammonia,
and 2-ketobutyrate. EC 4.4.1.1.;
MeSH synonym : gamma cystathionase; cysteine desulfhydrase; gamma-cystathionase; homoserine dehydratase; cystathionase; cystine desulfohydrolase; dehydratase, homoserine; cystine desulfhydrase; gamma-lyase, cystathionine; desulfohydrolase, cystine; desulfhydrase, cystine; desulfhydrase, cysteine; homoserine deaminase; deaminase, homoserine; cystathionine gamma lyase;
MeSH CAS label : L-Cystathionine cysteine-lyase (deaminating);
MeSH Related Number : 9012-96-8 (CAS RN);
Registry Number MeSH : EC 4.4.1.1;
MeSH annotation : /defic: consider also CYSTATHIONINE /urine (IM) AMINO ACID METABOLISM, INBORN ERRORS
(IM);
Wikipedia link : https://en.wikipedia.org/wiki/Cystathionine gamma-lyase;
Is substance : O;
UNII : EC 4.4.1.1;
Origin ID : D003542;
UMLS CUI : C0010642;
Allowable qualifiers
Indexing information
Record concept(s)
Related MeSH Supplementary Concept(s)
See also (suggested by CISMeF)
Semantic type(s)
UMLS correspondences (same concept)
A multifunctional pyridoxal phosphate enzyme. In the final step in the biosynthesis
of cysteine it catalyzes the cleavage of cystathionine to yield cysteine, ammonia,
and 2-ketobutyrate. EC 4.4.1.1.
http://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=FR&Expert=212
2006
France
French
rare diseases
cystathionine gamma-lyase
cystathionine
gamma-cystathionase deficiency
hyperhomocysteinemia
scientific and technical information
---