Preferred Label : cystathionine gamma-lyase;

MeSH definition : A multifunctional pyridoxal phosphate enzyme. In the final step in the biosynthesis of cysteine it catalyzes the cleavage of cystathionine to yield cysteine, ammonia, and 2-ketobutyrate. EC 4.4.1.1.;

MeSH synonym : gamma cystathionase; cysteine desulfhydrase; gamma-cystathionase; homoserine dehydratase; cystathionase; cystine desulfohydrolase; dehydratase, homoserine; cystine desulfhydrase; gamma-lyase, cystathionine; desulfohydrolase, cystine; desulfhydrase, cystine; desulfhydrase, cysteine; homoserine deaminase; deaminase, homoserine; cystathionine gamma lyase;

MeSH CAS label : L-Cystathionine cysteine-lyase (deaminating);

MeSH Related Number : 9012-96-8 (CAS RN);

Registry Number MeSH : EC 4.4.1.1;

MeSH annotation : /defic: consider also CYSTATHIONINE /urine (IM) AMINO ACID METABOLISM, INBORN ERRORS (IM);

Wikipedia link : https://en.wikipedia.org/wiki/Cystathionine gamma-lyase;

Is substance : O;

UNII : EC 4.4.1.1;

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A multifunctional pyridoxal phosphate enzyme. In the final step in the biosynthesis of cysteine it catalyzes the cleavage of cystathionine to yield cysteine, ammonia, and 2-ketobutyrate. EC 4.4.1.1.

http://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=FR&Expert=212
2006
France
French
rare diseases
cystathionine gamma-lyase
cystathionine
gamma-cystathionase deficiency
hyperhomocysteinemia
scientific and technical information

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02/05/2025


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