Other specified disorders involving the immune mechanism, not elsewhere classified

Preferred Label : Other specified disorders involving the immune mechanism, not elsewhere classified;

Diag associé à un acte (%) : 83.6;

Autres : 1;

CMA : 2;

Source : OMS;

Date de début : 01/01/1997;

Details

Origin ID

D898;

UMLS CUI

C0869046;

Orphanet concepts
- Autoimmune hemolytic anemia-autoimmune thrombocytopenia-primary immunodeficiency syndrome [ORDO Disease]
- Autoinflammation-PLCG2-associated antibody deficiency-immune dysregulation [ORDO Disease]
- Autoinflammatory syndrome with pyogenic bacterial infection and amylopectinosis [ORDO Disease]
- Blau syndrome [ORDO Disease]
- CAR T cell therapy-associated cytokine release syndrome [ORDO Disease]
- CEBPE-associated autoinflammation-immunodeficiency-neutrophil dysfunction syndrome [ORDO Disease]
- Corticosteroid-sensitive aseptic abscess syndrome [ORDO Disease]
- FADD-related immunodeficiency [ORDO Disease]
- Heavy chain deposition disease [ORDO Disease]
- Hereditary pediatric Behçet-like disease [ORDO Disease]
- Immunodeficiency due to CD25 deficiency [ORDO Disease]
- Infantile-onset periodic fever-panniculitis-dermatosis syndrome [ORDO Disease]
- Interstitial granulomatous dermatitis with arthritis [ORDO Disease]
- Light and heavy chain deposition disease [ORDO Disease]
- Light chain deposition disease [ORDO Disease]
- MAGIC syndrome [ORDO Disease]
- NLRC4-related familial cold autoinflammatory syndrome [ORDO Disease]
- Non-amyloid monoclonal immunoglobulin deposition disease [ORDO Disease]
- Proteasome-associated autoinflammatory syndrome [ORDO Disease]
- Pyogenic arthritis-pyoderma gangrenosum-acne syndrome [ORDO Disease]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
Validated automatic mappings to BTNT
- Cryopyrin-associated periodic syndromes [ICD-11 Subcategory]
- Familial Mediterranean fever [ICD-11 Subcategory]
- Hepatic veno-occlusive disease - immunodeficiency syndrome [ICD-11 Sub-sub category]
- Immune dysregulation syndromes with hypopigmentation [ICD-11 Sub-sub category]

Keyword's position in hierarchy(ies) :

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