Hepatic veno-occlusive disease - immunodeficiency syndrome

ICD-11 code : 4A01.33;

Preferred Label : Hepatic veno-occlusive disease - immunodeficiency syndrome;

ICD-11 definition : Hepatic veno-occlusive disease - immunodeficiency syndrome is characterized by the association of severe hypogammaglobulinemia, combined T and B cell immunodeficiency, absent lymph node germinal centers, absent tissue plasma cells and hepatic veno-occlusive disease.;

ICD-11 synonym : VODI syndrome; VODI - [Veno-occlusive disease immunodeficiency] syndrome;

CISMeF acronym : VODI;

Details

Origin ID

712514250;

UMLS CUI

C1856128;

Currated CISMeF NLP mapping
- Hepatic veno-occlusive disease with immunodeficiency syndrome (disorder) [SNOMED CT concept]
- Hepatic veno-occlusive disease-immunodeficiency syndrome [ORDO Disease]
- Hepatic venoocclusive disease with immunodeficiency [MeSH concept]
- Hepatic venoocclusive disease with immunodeficiency [OMIM Phenotype]
- hepatic venoocclusive disease with immunodeficiency [MeSH Supplementary Concept]
- hepatic venoocclusive disease with immunodeficiency [DO Concept]
ICD-10 Mapping
- Other specified disorders involving the immune mechanism, not elsewhere classified [ICD-10 Sub-category]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
UMLS correspondences (same concept)
- Hepatic veno-occlusive disease-immunodeficiency syndrome [ORDO Disease]
- Hepatic venoocclusive disease with immunodeficiency [OMIM Phenotype]
- Hepatic venoocclusive disease with immunodeficiency [MeSH concept]
- hepatic venoocclusive disease with immunodeficiency [MeSH Supplementary Concept]
Validated automatic mappings to NTBT
- Disorder of immune function (disorder) [SNOMED CT concept]
- Other specified disorders involving the immune mechanism, not elsewhere classified [ICD-10 Sub-category]

Keyword's position in hierarchy(ies) :

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