" /> Hereditary ATTR amyloidosis - CISMeF





ICD-11 code : 5D00.20;

Preferred Label : Hereditary ATTR amyloidosis;

ICD-11 synonym : Andrade type amyloid polyneuropathy; hereditary amyloid polyneuropathy Portuguese type; Portuguese amyloidosis; Portuguese amyloid polyneuropathy; polyneuropathy in amyloidosis; Paramyloidosis; Wohlwill-Corino Andrade syndrome; Transthyretin-related amyloidosis; familial amyloid polyneuropathy; Andrade syndrome; hereditary neuropathic amyloidosis Type 1; Corino de Andrade paramyloidosis; Swiss type amyloid polyneuropathy; type I familial amyloid polyneuropathy; type II familial amyloid polyneuropathy; familial polyneuropathic amyloidosis; familial amyloid neuropathy, Portuguese type; Neuropathic heredofamilial amyloidosis; familial neuropathic amyloidosis; FAP - [familial amyloid polyneuropathy]; amyloid polyneuropathy type 1; Portuguese polyneuritic amyloidosis; Japanese type amyloid polyneuropathy; familial amyloid neuropathy, Andrade type; Swedish type amyloid polyneuropathy; Portuguese type familial amyloid neuropathy; AF type amyloidosis; amyloidosis Type 1; amyloid polyneuropathy;

ICD-11 acronym : FAP;

ICD-11 inclusion : familial amyloid polyneuropathy, 30 met-for-val; Portuguese type amyloid polyneuropathy;

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31/07/2025


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