" /> Hereditary haemorrhagic telangiectasia - CISMeF





ICD-11 code : LA90.00;

Preferred Label : Hereditary haemorrhagic telangiectasia;

ICD-11 definition : Rendu-Osler-Weber disease, also called hereditary hemorrhagic telangiectasia (HHT), is a genetic disorder of angiogenesis leading to arteriovenous dilatations: cutaneo-mucosal hemorrhagic telangiectasias and visceral shunting.;

ICD-11 synonym : Osler-Weber-Rendu disease; Rendu-Osler-Weber disease; Osler haemorrhagic telangiectasia syndrome; HHT - [hereditary haemorrhagic telangiectasia];

ICD-11 acronym : HHT;

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Rendu-Osler-Weber disease, also called hereditary hemorrhagic telangiectasia (HHT), is a genetic disorder of angiogenesis leading to arteriovenous dilatations: cutaneo-mucosal hemorrhagic telangiectasias and visceral shunting.

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27/07/2025


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