" /> Homozygous or compound heterozygous alpha0 thalassaemia - CISMeF





ICD-11 code : 3A50.03;

Preferred Label : Homozygous or compound heterozygous alpha0 thalassaemia;

ICD-11 definition : Hb Bart's hydrops fetalis is the most severe form of alpha-thalassemia and is almost always lethal. It is characterized by fetal onset of generalized edema, pleural and pericardial effusions, and severe hypochromic anemia.;

ICD-11 synonym : Alpha thalassaemia hydrops fetalis; Hb Bart's hydrops fetalis; Haemoglobin Bart hydrops fetalis;

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Hb Bart's hydrops fetalis is the most severe form of alpha-thalassemia and is almost always lethal. It is characterized by fetal onset of generalized edema, pleural and pericardial effusions, and severe hypochromic anemia.

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07/07/2025


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